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Acta Haematologica Polonica最新文献

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Mediastinal tumor: thymoma or lymphoma? 纵隔肿瘤:胸腺瘤还是淋巴瘤?
Acta Haematologica Polonica Pub Date : 2023-10-10 DOI: 10.5603/ahp.95457
Barbara Tejza, Elżbieta Grześk
{"title":"Mediastinal tumor: thymoma or lymphoma?","authors":"Barbara Tejza, Elżbieta Grześk","doi":"10.5603/ahp.95457","DOIUrl":"https://doi.org/10.5603/ahp.95457","url":null,"abstract":"","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136294118","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Towards the future of Polish hematology: perspectives after 31st Meeting of Polish Society of Hematologists and Transfusiologists 迈向波兰血液学的未来:波兰血液学家和输血学家协会第31次会议后的观点
Acta Haematologica Polonica Pub Date : 2023-10-10 DOI: 10.5603/ahp.97715
Jan Styczyński
{"title":"Towards the future of Polish hematology: perspectives after 31st Meeting of Polish Society of Hematologists and Transfusiologists","authors":"Jan Styczyński","doi":"10.5603/ahp.97715","DOIUrl":"https://doi.org/10.5603/ahp.97715","url":null,"abstract":"The biannual Congress of the Polish Society of Hematology and Transfusion Medicine is the most important event for all those involved in hematology and transfusiology. Between 14 and 16 September 2023, almost 1,300 attendees met in Katowice to discuss progress in these disciplines. Nowadays, the results of therapy of hematological malignancies in Poland are almost the same as the European average value. This is the result of hard work by the national working groups as well as international collaboration. Since 2021, Polish hematology has achieved great progress in therapy with the use of chimeric antigen receptor T-cell therapy. Also, a number of new compounds for hematological disorders, and supportive therapy, have been introduced in Poland, either within clinical trials or reimbursed by the National Health Fund. Even so, many patients still suffer unmet medical needs. Several important compounds, already licensed, are awaiting reimbursement. New cellular technologies are in the pipeline. The reimbursement of more therapies is desired, and further progress in diagnostic and therapeutic methods is required.","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136294119","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Prophylaxis with tenofovir in hepatitis-associated severe aplastic anemia treated with hematopoietic cell transplantation 替诺福韦预防造血细胞移植治疗肝炎相关性严重再生障碍性贫血
Acta Haematologica Polonica Pub Date : 2023-10-10 DOI: 10.5603/ahp.96892
Melissa Prodisteanu, Artur Tumiński, Monika Richert-Przygońska, Robert Dębski, Krzysztof Czyżewski
{"title":"Prophylaxis with tenofovir in hepatitis-associated severe aplastic anemia treated with hematopoietic cell transplantation","authors":"Melissa Prodisteanu, Artur Tumiński, Monika Richert-Przygońska, Robert Dębski, Krzysztof Czyżewski","doi":"10.5603/ahp.96892","DOIUrl":"https://doi.org/10.5603/ahp.96892","url":null,"abstract":"","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136356746","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Impact of molecular status on clinical management in children with histiocytosis treated according to POL HISTIO project 分子状态对POL HISTIO项目治疗的组织细胞增多症患儿临床管理的影响
Acta Haematologica Polonica Pub Date : 2023-10-05 DOI: 10.5603/ahp.95452
Anna Raciborska, Zofia Małas, Andrzej Tysarowski, Katarzyna Seliga, Katarzyna Machnik, Jadwiga Wecławek-Tompol, Katarzyna Derwich, Iwona Ruranska, Katarzyna Muszyńska-Rosłan, Elżbieta Michalak, Wanda Badowska, Grażyna Karolczyk, Radosław Chaber, Katarzyna Drabko, Carlos Rodriguez-Galindo
{"title":"Impact of molecular status on clinical management in children with histiocytosis treated according to POL HISTIO project","authors":"Anna Raciborska, Zofia Małas, Andrzej Tysarowski, Katarzyna Seliga, Katarzyna Machnik, Jadwiga Wecławek-Tompol, Katarzyna Derwich, Iwona Ruranska, Katarzyna Muszyńska-Rosłan, Elżbieta Michalak, Wanda Badowska, Grażyna Karolczyk, Radosław Chaber, Katarzyna Drabko, Carlos Rodriguez-Galindo","doi":"10.5603/ahp.95452","DOIUrl":"https://doi.org/10.5603/ahp.95452","url":null,"abstract":"","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135480827","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Myelodysplastic syndrome and pulmonary alveolar proteinosis in a 6-year-old girl with mutation of the ZBTB24 gene 6岁女孩ZBTB24基因突变的骨髓增生异常综合征和肺泡蛋白沉积症
Acta Haematologica Polonica Pub Date : 2023-10-05 DOI: 10.5603/ahp.95371
Piotr Homa, Wojciech Homa, Urszula Janiuk, Magdalena Cienkusz, Teresa Bielecka, Katarzyna Krenke, Katarzyna Drabko
{"title":"Myelodysplastic syndrome and pulmonary alveolar proteinosis in a 6-year-old girl with mutation of the ZBTB24 gene","authors":"Piotr Homa, Wojciech Homa, Urszula Janiuk, Magdalena Cienkusz, Teresa Bielecka, Katarzyna Krenke, Katarzyna Drabko","doi":"10.5603/ahp.95371","DOIUrl":"https://doi.org/10.5603/ahp.95371","url":null,"abstract":"In this article, we report a case of a 6-year-old girl, initially diagnosed with myelodysplastic syndrome (MDS), who presented a compound and uncharacteristic set of symptoms that included low level of lymphocytes, hypogammaglobulinemia, developmental delay and facial anomalies. An unconventional course of the disease gave premises to extended genetic diagnostic using next-generation sequencing, that provided the result of heterozygous ZBTB24 c.[1222T > G] cysteine-to-glycine missense mutation, which is characteristic of immunodeficiency, centromeric instability and facial dysmorphism syndrome type 2 (ICF2). During the treatment of hematologic disorders, the patient underwent allogenic stem cell transplantation (allo-HSCT). After performing allo-HSCT, another rare syndrome has been developed in form of pulmonary alveolar proteinosis (PAP). In this paper, we describe the whole diagnostic process, usage of drugs that include immunoglobulins, rituximab, steroids, azathioprine and performed therapeutic procedures, such as allo-HSCT and lung lavages. The unique value of this case lays in the coexistence of several rare diseases and response of the patient to multi-thread treatment.","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135435855","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Very late relapse of ALL after 14 years: treatment with CAR-T cells 急性淋巴细胞白血病14年后晚期复发:CAR-T细胞治疗
Acta Haematologica Polonica Pub Date : 2023-10-05 DOI: 10.5603/ahp.96850
Monika Richert-Przygońska, Krzysztof Czyżewski, Robert Dębski, Małgorzata Kubicka, Beata Kurylo-Rafińka, Agnieszka Majk, Ewa Dembna, Łukasz Ledziński, Ewa Marquardt, Honorata Mlicka, Katarzyna Gągola, Jan Styczyński
{"title":"Very late relapse of ALL after 14 years: treatment with CAR-T cells","authors":"Monika Richert-Przygońska, Krzysztof Czyżewski, Robert Dębski, Małgorzata Kubicka, Beata Kurylo-Rafińka, Agnieszka Majk, Ewa Dembna, Łukasz Ledziński, Ewa Marquardt, Honorata Mlicka, Katarzyna Gągola, Jan Styczyński","doi":"10.5603/ahp.96850","DOIUrl":"https://doi.org/10.5603/ahp.96850","url":null,"abstract":"","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135482517","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Sclerodermatous manifestation of chronic graft versus host disease: therapy challenges 慢性移植物抗宿主病的硬化性表现:治疗挑战
Acta Haematologica Polonica Pub Date : 2023-10-05 DOI: 10.5603/ahp.96817
Monika Richert-Przygońska, Magdalena Milewska, Robert Dębski, Joanna Cisek, Krzysztof Czyżewski
{"title":"Sclerodermatous manifestation of chronic graft versus host disease: therapy challenges","authors":"Monika Richert-Przygońska, Magdalena Milewska, Robert Dębski, Joanna Cisek, Krzysztof Czyżewski","doi":"10.5603/ahp.96817","DOIUrl":"https://doi.org/10.5603/ahp.96817","url":null,"abstract":"Chronic graft versus host disease (cGHVD) is one of the most serious complications after allogeneic hematopoietic cell transplantation (allo-HCT). It varies in between patients, often leading to systemic and functional limitations. It can be challenging considering the heterogeneity of patients. The objective of this paper is to present clinical aspects of sclerodermatous manifestation of cGVHD as a complication of allo-HCT in pediatric patients. We diagnosed three patients with different sclerodermatous skin involvement and cGVHD features. The treatment applied varied among patients and was based on current available standards of care. We analyzed effectiveness of systemic steroid therapy, extracorporeal photopheresis and ruxolitinib. In conclusion, all patients achieved improvement in skin leasions and quality of life, based on the individualized treatment approach.","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134975025","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Dyskeratosis congenita as a multifaceted bone marrow disorder 先天性角化不良是一种多面性骨髓疾病
Acta Haematologica Polonica Pub Date : 2023-10-03 DOI: 10.5603/ahp.95640
Maciej Mazurek, Joanna Madzio, Wojciech Młynarski
{"title":"Dyskeratosis congenita as a multifaceted bone marrow disorder","authors":"Maciej Mazurek, Joanna Madzio, Wojciech Młynarski","doi":"10.5603/ahp.95640","DOIUrl":"https://doi.org/10.5603/ahp.95640","url":null,"abstract":"Dyskeratosis congenita (DC) is a rare multisystem clinical entity caused by genetic mutations associated with telomere biology disorder. The symptoms include bone marrow dysfunction as well as skin and mucosal abnormalities. In severe cases, DC is characterized by high mortality rates among children. In milder subtypes, it is less detectable in adults, due to the occurrence of cryptic forms of the disease. To date, more than 15 mutated genes have been shown as causative for DC. The aim of this study was to provide a brief description of the currently known clinical and genetic characteristics of DC, and to elucidate the molecular pathogenesis.","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135695705","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Hematology and transfusion medicine journal of pediatric and adult diseases: we all are readers, authors and reviewers 血液学与输血医学儿科与成人疾病杂志:我们都是读者、作者和审稿人
Acta Haematologica Polonica Pub Date : 2023-10-03 DOI: 10.5603/ahp.97593
Jan Styczyński
{"title":"Hematology and transfusion medicine journal of pediatric and adult diseases: we all are readers, authors and reviewers","authors":"Jan Styczyński","doi":"10.5603/ahp.97593","DOIUrl":"https://doi.org/10.5603/ahp.97593","url":null,"abstract":"","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135696249","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Acute pancreatitis in children with acute lymphoblastic leukemia 急性淋巴细胞白血病患儿的急性胰腺炎
Acta Haematologica Polonica Pub Date : 2023-10-03 DOI: 10.5603/ahp.95319
Alicja Maziarczyk, Maciej Lambach, Paulina Kura, Monika Lejman, Joanna Zawitkowska
{"title":"Acute pancreatitis in children with acute lymphoblastic leukemia","authors":"Alicja Maziarczyk, Maciej Lambach, Paulina Kura, Monika Lejman, Joanna Zawitkowska","doi":"10.5603/ahp.95319","DOIUrl":"https://doi.org/10.5603/ahp.95319","url":null,"abstract":"One of the most common causes of acute pancreatitis in children is medications. These include L-asparaginase, glucocorticoids and 6-mercaptopurine, which are widely used in the therapy of acute lymphoblastic leukemia (ALL). When L-asparaginase and glucocorticoids are administered together, blood triglyceride levels increase, which consequently further enhances the risk of pancreatitis. Therefore, acute pancreatitis is a common side effect of ALL treatment, present in 2.3–11% of pediatric patients. The aim of this paper was to review studies on acute pancreatitis in children with ALL and to assess potential risk factors, treatment outcomes and recurrence of this condition. Based on the studies conducted, we found potential risk factors, other than the drugs mentioned above, to be the patient’s age at diagnosis, obesity, the type of L-asparaginase administered, and the cumulative or peak dose of L-asparaginase or other drug used. Fortunately, the course of pancreatitis is usually mild to moderate, and the treatment is mainly symptomatic. Moreover, a successful treatment option may be octreotide. As children who have received less than 25 weeks of L-asparaginase therapy have presented with inferior outcomes, it seems reasonable to reintroduce this drug into ALL treatment after an episode of pancreatitis. The incidence of recurrent pancreatitis after re-treatment with L-asparaginase varies depending on the study. Unfortunately, the outcomes for children who develop acute pancreatitis during ALL treatment are usually worse compared to children without an acute pancreatitis history, but the results remain inconclusive. Further research is needed to assess the management of acute pancreatitis, and to minimize the worsening of ALL outcomes among these patients.","PeriodicalId":35805,"journal":{"name":"Acta Haematologica Polonica","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135696517","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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