{"title":"Introduction: Nomenclature and Classification","authors":"J. Jennette, R. Falk","doi":"10.1007/978-3-030-02239-6_1","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_1","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"1939 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128740716","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Activity and Damage","authors":"R. Luqmani","doi":"10.1007/978-3-030-02239-6_5","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_5","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"52 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115231611","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Genetics of ANCA-Associated Vasculitis","authors":"F. Alberici, P. Lyons, D. Martorana","doi":"10.1007/978-3-030-02239-6_2","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_2","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"109 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124848304","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Emmi C. Salvarani, R. Sinico, M. D’Elios, M. Rizzi
{"title":"Humoral Primary Immunodeficiencies","authors":"Emmi C. Salvarani, R. Sinico, M. D’Elios, M. Rizzi","doi":"10.1007/978-3-319-91785-6","DOIUrl":"https://doi.org/10.1007/978-3-319-91785-6","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"139 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121320809","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"ANCA-Associated Vasculitis—ENT Involvement","authors":"T. Matteo, G. Andrea, R. Teggi","doi":"10.1007/978-3-030-02239-6_9","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_9","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"41 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121390211","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Prognosis and Outcomes of ANCA-Associated Vasculitis","authors":"D. Jayne","doi":"10.1007/978-3-030-02239-6_16","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_16","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"40 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129489935","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Eosinophilic Granulomatosis with Polyangiitis (EGPA, Churg–Strauss)","authors":"Y. Nguyen, L. Guillevin","doi":"10.1007/978-3-030-02239-6_6","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_6","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"45 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129858650","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Miscellaneous Organ Involvement in ANCA-Associated Vasculitis","authors":"Giorgio Trivioli, A. Vaglio","doi":"10.1007/978-3-030-02239-6_15","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_15","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"193 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121716547","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Etiopathogenesis of ANCA-Associated Vasculitis","authors":"D. Sterlin, A. Mathian, M. Miyara","doi":"10.1007/978-3-030-02239-6_3","DOIUrl":"https://doi.org/10.1007/978-3-030-02239-6_3","url":null,"abstract":"","PeriodicalId":313096,"journal":{"name":"Rare Diseases of the Immune System","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122281747","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}