10.03 - Adult CF最新文献

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The effect of triple therapy cystic fibrosis transmembrane conductance regulator (CFTR) modulation on anxiety in people with cystic fibrosis 三联疗法囊性纤维化跨膜传导调节剂(CFTR)对囊性纤维化患者焦虑的影响
10.03 - Adult CF Pub Date : 2022-09-04 DOI: 10.1183/13993003.congress-2022.2283
O. O’Carroll, C. Mc Keown, J. Bell, T. Nicholson, C. Gallagher, E. Mc Kone
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引用次数: 0
Triple CFTR modulator therapy is associated with improved endocrine pancreatic function in patients with cystic fibrosis 三重CFTR调节剂治疗可改善囊性纤维化患者的内分泌胰腺功能
10.03 - Adult CF Pub Date : 2022-09-04 DOI: 10.1183/13993003.congress-2022.3750
C. Steinack, T. Gaisl, F. Beuschlein, S. Macé Matthew, M. Ernst
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引用次数: 0
Real-world effects of lumacaftor/ivacaftor (LUM/IVA) in people with cystic fibrosis (pwCF): final results of a long-term safety study using US CF Foundation Patient Registry and UK CF Patient Registry data lumacaftor/ivacaftor (LUM/IVA)对囊性纤维化(pwCF)患者的实际影响:一项使用美国CF基金会患者登记处和英国CF患者登记处数据的长期安全性研究的最终结果
10.03 - Adult CF Pub Date : 2022-09-04 DOI: 10.1183/13993003.congress-2022.712
C. Kim, S. Tian, R. Zahigian, A. Elbert, S. Charman, S. Carr, D. Nazareth
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引用次数: 0
Early-infection Pseudomonas aeruginosa isolates from Cystic Fibrosis patients have high levels of LasB elastase activity 从囊性纤维化患者分离的早期感染铜绿假单胞菌具有高水平的LasB弹性酶活性
10.03 - Adult CF Pub Date : 2022-09-04 DOI: 10.1183/13993003.congress-2022.921
A. Llanos, P. Achard, C. Lozano, J. Bousquet, M. Zalacain, H. Guet-Revillet, M. Murris‐Espin, M. Mittaine, M. Everett
{"title":"Early-infection Pseudomonas aeruginosa isolates from Cystic Fibrosis patients have high levels of LasB elastase activity","authors":"A. Llanos, P. Achard, C. Lozano, J. Bousquet, M. Zalacain, H. Guet-Revillet, M. Murris‐Espin, M. Mittaine, M. Everett","doi":"10.1183/13993003.congress-2022.921","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.921","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125614028","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Elexacaftor tezacaftor ivacaftor therapy alters plasma sphingolipid profiles in people with cystic fibrosis elexaftor tezacaftor ivacaftor治疗可改变囊性纤维化患者血浆鞘脂谱
10.03 - Adult CF Pub Date : 2022-09-04 DOI: 10.1183/13993003.congress-2022.240
D. Westhölter, F. Schumacher, N. Wülfinghoff, S. Sutharsan, S. Strassburg, B. Kleuser, P. A. Horn, S. Reuter, E. Gulbins, C. Taube, M. Welsner
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引用次数: 0
Modelling the behaviour of the mucus layer in the small airways 模拟小气道中黏液层的行为
10.03 - Adult CF Pub Date : 2022-09-04 DOI: 10.1183/13993003.congress-2022.2611
J. Shemilt, A. Horsley, O. Jensen, A. Thompson, C. Whitfield
{"title":"Modelling the behaviour of the mucus layer in the small airways","authors":"J. Shemilt, A. Horsley, O. Jensen, A. Thompson, C. Whitfield","doi":"10.1183/13993003.congress-2022.2611","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.2611","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125060395","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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