10.03 - Adult CFPub Date : 2022-09-04DOI: 10.1183/13993003.congress-2022.2283
O. O’Carroll, C. Mc Keown, J. Bell, T. Nicholson, C. Gallagher, E. Mc Kone
{"title":"The effect of triple therapy cystic fibrosis transmembrane conductance regulator (CFTR) modulation on anxiety in people with cystic fibrosis","authors":"O. O’Carroll, C. Mc Keown, J. Bell, T. Nicholson, C. Gallagher, E. Mc Kone","doi":"10.1183/13993003.congress-2022.2283","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.2283","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"2 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115681655","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
10.03 - Adult CFPub Date : 2022-09-04DOI: 10.1183/13993003.congress-2022.3750
C. Steinack, T. Gaisl, F. Beuschlein, S. Macé Matthew, M. Ernst
{"title":"Triple CFTR modulator therapy is associated with improved endocrine pancreatic function in patients with cystic fibrosis","authors":"C. Steinack, T. Gaisl, F. Beuschlein, S. Macé Matthew, M. Ernst","doi":"10.1183/13993003.congress-2022.3750","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.3750","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"15 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134300300","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
10.03 - Adult CFPub Date : 2022-09-04DOI: 10.1183/13993003.congress-2022.712
C. Kim, S. Tian, R. Zahigian, A. Elbert, S. Charman, S. Carr, D. Nazareth
{"title":"Real-world effects of lumacaftor/ivacaftor (LUM/IVA) in people with cystic fibrosis (pwCF): final results of a long-term safety study using US CF Foundation Patient Registry and UK CF Patient Registry data","authors":"C. Kim, S. Tian, R. Zahigian, A. Elbert, S. Charman, S. Carr, D. Nazareth","doi":"10.1183/13993003.congress-2022.712","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.712","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"8 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122013380","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
10.03 - Adult CFPub Date : 2022-09-04DOI: 10.1183/13993003.congress-2022.921
A. Llanos, P. Achard, C. Lozano, J. Bousquet, M. Zalacain, H. Guet-Revillet, M. Murris‐Espin, M. Mittaine, M. Everett
{"title":"Early-infection Pseudomonas aeruginosa isolates from Cystic Fibrosis patients have high levels of LasB elastase activity","authors":"A. Llanos, P. Achard, C. Lozano, J. Bousquet, M. Zalacain, H. Guet-Revillet, M. Murris‐Espin, M. Mittaine, M. Everett","doi":"10.1183/13993003.congress-2022.921","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.921","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125614028","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
10.03 - Adult CFPub Date : 2022-09-04DOI: 10.1183/13993003.congress-2022.240
D. Westhölter, F. Schumacher, N. Wülfinghoff, S. Sutharsan, S. Strassburg, B. Kleuser, P. A. Horn, S. Reuter, E. Gulbins, C. Taube, M. Welsner
{"title":"Elexacaftor tezacaftor ivacaftor therapy alters plasma sphingolipid profiles in people with cystic fibrosis","authors":"D. Westhölter, F. Schumacher, N. Wülfinghoff, S. Sutharsan, S. Strassburg, B. Kleuser, P. A. Horn, S. Reuter, E. Gulbins, C. Taube, M. Welsner","doi":"10.1183/13993003.congress-2022.240","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.240","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"28 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130175957","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
10.03 - Adult CFPub Date : 2022-09-04DOI: 10.1183/13993003.congress-2022.2611
J. Shemilt, A. Horsley, O. Jensen, A. Thompson, C. Whitfield
{"title":"Modelling the behaviour of the mucus layer in the small airways","authors":"J. Shemilt, A. Horsley, O. Jensen, A. Thompson, C. Whitfield","doi":"10.1183/13993003.congress-2022.2611","DOIUrl":"https://doi.org/10.1183/13993003.congress-2022.2611","url":null,"abstract":"","PeriodicalId":306536,"journal":{"name":"10.03 - Adult CF","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-09-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125060395","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}