{"title":"Large Congenital Epigastric Hernia with DiGeorge Syndrome: A Case Report","authors":"Hee Ju Kim, J. Chung","doi":"10.13029/aps.2021.27.1.22","DOIUrl":"https://doi.org/10.13029/aps.2021.27.1.22","url":null,"abstract":"","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"96 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"132878829","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
B. Song, Suk-Bae Moon, G. Chae, Sung-Bae Park, S. Hong, Yang Hee Kim, Sang-Ji Choi, Hwansoo Kim
{"title":"CT Findings that Indicate Pediatric Appendicitis: Lessons from Negative Appendectomies","authors":"B. Song, Suk-Bae Moon, G. Chae, Sung-Bae Park, S. Hong, Yang Hee Kim, Sang-Ji Choi, Hwansoo Kim","doi":"10.13029/aps.2021.27.1.15","DOIUrl":"https://doi.org/10.13029/aps.2021.27.1.15","url":null,"abstract":"Purpose: Abdominal computed tomography (ACT) is widely used to diagnose appendicitis in children. Despite its high sensitivity and specificity, “negative appendectomies” still occur when the patient undergoes surgery but the final pathologic diagnosis does not support appendicitis. The aim of this study is to determine which findings support true appendicitis in patients with unclear findings on preoperative ACT. Methods: We performed a retrospective review of the records of 620 pediatric patients who underwent surgery for acute appendicitis between January 1, 2007 and December 31, 2020. We re-reviewed the scans in 101 patients who were deemed to have unclear preoperative findings on ACT, looking for the following features: periappendiceal fat infiltration, periappendiceal fluid collection, appendiceal wall thickening, appendiceal gas, and right lower quadrant lymphadenopathy. We then compared the presence of these features between patients with true appendicitis and those who underwent negative appendectomy. Results: The presence of an enlarged appendix, with a maximum diameter of more than 8 mm, and the presence of periappendiceal fat infiltration were associated with true appendicitis. Conclusion: If ACT findings are unclear in a patient with suspected acute appendicitis, the presence of an enlarged appendix and periappendiceal fat infiltration should be assessed to differentiate those with true appendicitis.","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"13 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126842627","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Kwang-Jin Lee, Suk-Bae Moon, Sang-Ji Choi, G. Chae, Sung-Bae Park, S. Hong, Yang Hee Kim, Hwansoo Kim
{"title":"Experiences of Preoperative COVID-19 Screening in Pediatric Patients in a Secondary Care Center","authors":"Kwang-Jin Lee, Suk-Bae Moon, Sang-Ji Choi, G. Chae, Sung-Bae Park, S. Hong, Yang Hee Kim, Hwansoo Kim","doi":"10.13029/aps.2021.27.1.1","DOIUrl":"https://doi.org/10.13029/aps.2021.27.1.1","url":null,"abstract":"","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"396 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123202226","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Bleeding Gastric Heterotopia of Cecal Diverticulum in an Adolescent: A Case Report","authors":"H. Seo, J. Kwak","doi":"10.13029/aps.2021.27.1.32","DOIUrl":"https://doi.org/10.13029/aps.2021.27.1.32","url":null,"abstract":"","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"11 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129400633","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Successful Multiteam Approach for Massive Jejunoileal Bleeding 10 Years after Gastrectomy for Spontaneous Gastric Perforation in Neonate: A Case Report","authors":"J. Jeong, I. Kim, Hyun Soo Kim, W. Kim, J. Hah","doi":"10.13029/aps.2021.27.1.27","DOIUrl":"https://doi.org/10.13029/aps.2021.27.1.27","url":null,"abstract":"","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"23 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133085011","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Haddad Syndrome: A Case of Congenital Central Hypoventilation Syndrome Combined with Hirschsprung Disease","authors":"So-young Jeong, H. Shin, Y. Jeong, Jin Kyu Kim","doi":"10.13029/aps.2020.26.2.72","DOIUrl":"https://doi.org/10.13029/aps.2020.26.2.72","url":null,"abstract":"Congenital central hypoventilation syndrome (CCHS) with Hirschsprung disease (HD), also known as Haddad syndrome, is an extremely rare disorder. Recent studies have identified the paired like homeobox 2b (PHOX2B) gene as the major gene involved in the development of CCHS. The syndrome is diagnosed when gene analysis confirms a mutation in the involved gene, but making an early diagnosis is difficult because of the rarity of the disease. In this study, we report the case of a newborn male with recurrent hypoventilation and bowel distension. HD was suspected on barium enema, and loop ileostomy was performed. After surgery, the abdominal symptoms gradually improved, but extubation was not possible owing to recurrent respiratory failure. These clinical manifestations were indicative of Haddad syndrome, and genetic testing confirmed the presence of a PHOX2B mutation. The patient was diagnosed with Haddad syndrome on the 11th day after birth.","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2020-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116957034","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Situs Inversus Totalis, Polysplenia and Annular Pancreas with Duodenal Obstruction: a Case Report of Bizarre Embryological Conundrum","authors":"Swapnil Pattanshetti, N. Peters, R. Samujh","doi":"10.13029/aps.2020.26.2.67","DOIUrl":"https://doi.org/10.13029/aps.2020.26.2.67","url":null,"abstract":"Situs inversus, polysplenia and annular pancreas are unusual anomalies individually, and are extremely rare in combination. A 3 years old boy presented with failure to thrive and symptoms of chronic upper gastrointestinal obstruction. After adequate radiological investigations, he was explored and managed with a duodeno-duodenostomy. and is doing well on a 1 year follow-up. The preoperative radiological assessment is of paramount importance, so as to avoid any intra-operative surprises.","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"75 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2020-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133458106","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Dayoung Ko, Changhoon Lee, J. Youn, Hee-Beom Yang, Hyun-Young Kim
{"title":"Do Children with Esophageal Atresia Show Worse Growth Outcomes?","authors":"Dayoung Ko, Changhoon Lee, J. Youn, Hee-Beom Yang, Hyun-Young Kim","doi":"10.13029/aps.2020.26.2.54","DOIUrl":"https://doi.org/10.13029/aps.2020.26.2.54","url":null,"abstract":"Purpose: Patients with esophageal atresia (EA) often have feeding problems due to esophageal dysmotility, gastroesophageal reflux, and dysphagia, which can delay growth in children. The purpose of this study was to investigate whether proper growth is achieved during the early childhood of patients with EA and to predict associated factors. Methods: Clinical data of patients with EA who underwent corrective surgery between 2014 and 2017 were collected retrospectively. We analyzed a total of 17 patients who were followed up for at least two years after surgery, except for patients with long-gap and type E EA. The median follow-up period was 979.0 months. We analyzed the weight, height, and weight-for-height (WFH) as z-scores. Linear regression analysis was performed to determine the factors affecting WFH at two years of age. Results: Of the 17 patients, 11 underwent open surgery and six underwent thoracoscopic surgery. The median time to full feeding was approximately 14 (range, 12.0–53.0) days. In patients with anastomotic stenosis, esophageal balloon dilatation was performed 1–6 times. There was no mortality in our study, and the median follow-up period was 979 days. The mean height was 49.0 cm, the mean weight at birth was 2.69 kg, and the z-scores were −0.55 and −1.44, respectively. The WFH z-score decreased from −1.66 at birth to −1.82 one week postoperatively; however, it improved to −0.2 after six months. In multivariate linear regression analysis, only WFH at birth was a significant variable for WFH at two years of age. Conclusion: Patients with EA tend to have lower weight and WFH at birth, which worsened after surgery; however, six months after surgery, both weight and WFH recovered to the 50th percentile. The factors that influence WFH at two years of age were significantly related to WFH at birth.","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"13 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2020-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127316657","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
G. Song, Jong Hyuk Yun, H. Jung, T. Ahn, M. Son, S. Han, S. Bae, S. Kim, M. Baek, Moon-Soo Lee
{"title":"Gastrointestinal Perforation Caused by Neodymium Magnet Toys: A Dangerous Foreign Body with Super-Strength","authors":"G. Song, Jong Hyuk Yun, H. Jung, T. Ahn, M. Son, S. Han, S. Bae, S. Kim, M. Baek, Moon-Soo Lee","doi":"10.13029/aps.2020.26.2.83","DOIUrl":"https://doi.org/10.13029/aps.2020.26.2.83","url":null,"abstract":"Ingestion of neodymium magnets can cause serious complications in children. Making the decision of treatment is difficult because of nonspecific clinical presentation. We report 2 unusual cases of multiple gastrointestinal perforations with closed loop caused by ingestion of multiple bead-shaped neodymium magnets, which are different from the case caused by ingestion of typical magnets. In the first case, the patient was a 2-year-old boy with multiple jejunal perforations. In the second case, the patient was a 19-month-old girl with gastric and proximal jejunal perforations. Patients presented mild and nonspecific symptoms. Exploratory laparotomy was performed, which led to an uneventful postoperative course in both cases. Popular magnet toys composed of small bead-shaped neodymium magnets have different characteristics from typical magnets. They are enough small to swallow easily with greater magnetic force than typical magnets. When multiple neodymium magnets are ingested, they can attract with greater strength across bowel loops, causing pressure necrosis, perforation. However, patients can only present mild and nonspecific symptoms at the time of visit hospital because perforation sites were sealed by magnets which attract each other with great force. Therefore, surgeons should have a high index of suspicion for gastrointestinal perforation in any patient who has ingested multiple magnets, particularly composed of neodymium, presenting with persistent nonspecific abdominal pain.","PeriodicalId":246042,"journal":{"name":"Advances in Pediatric Surgery","volume":"10 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2020-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125294785","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}