Minamura Takeichi, Mari Kurokawa, Shinichi Shiona, Y. Kaku
{"title":"A case of IgA vasculitis, acute glomerulonephritis and Henoch-Schönlein purpura nephritis: successional complications of streptococcal infection","authors":"Minamura Takeichi, Mari Kurokawa, Shinichi Shiona, Y. Kaku","doi":"10.3165/jjpn.cr.2020.0176","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2020.0176","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115619013","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Yooka Nam, R. Hiramoto, S. Shinozuka, S. Matsumoto, H. Eguchi, B. Akikusa
{"title":"Efficacy and safety of long-term administration of mycophenolate mofetil after rituximab in patients with refractory nephrotic syndrome","authors":"Yooka Nam, R. Hiramoto, S. Shinozuka, S. Matsumoto, H. Eguchi, B. Akikusa","doi":"10.3165/jjpn.oa.2022.0203","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2022.0203","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"180 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122520358","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
R. Ohyama, Mayu Nakagawa, T. Morishita, Shota Endo, Y. Takemasa, Yuta Onuki, Koji Sakuraya, H. Murakami, S. Fujinaga
{"title":"A 3-year-old boy with steroid-resistant nephrotic syndrome who was diagnosed with severe lupus nephritis one year later: a case report","authors":"R. Ohyama, Mayu Nakagawa, T. Morishita, Shota Endo, Y. Takemasa, Yuta Onuki, Koji Sakuraya, H. Murakami, S. Fujinaga","doi":"10.3165/jjpn.cr.2021.0202","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2021.0202","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129682011","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Clinical sequencing for nephrologists","authors":"N. Morisada, Kana Hiromoto","doi":"10.3165/jjpn.rv.2021.0002","DOIUrl":"https://doi.org/10.3165/jjpn.rv.2021.0002","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133966447","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Koji Sakuraya, A. Endo, Akina Matsuda, Hiroki Miyano, Hiroaki Gonda, Masahito Saito, Akira Mizutani, Y. Ohtomo
{"title":"Assessment of skills in pediatric renal urology procedures among young pediatricians","authors":"Koji Sakuraya, A. Endo, Akina Matsuda, Hiroki Miyano, Hiroaki Gonda, Masahito Saito, Akira Mizutani, Y. Ohtomo","doi":"10.3165/jjpn.oa.2021.0197","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2021.0197","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"200 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128592421","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Y. Inaba, R. Hamada, Ryoko Harada, Junya Hashimoto, Wataru Kubota, Chikako Terano, N. Mikami, H. Hataya, Junpei Kuroda, Uiko Mizuguchi, R. Kakinuma, Masatoshi Kondo, T. Kono, M. Honda
{"title":"Characteristic ultrasonic view of the kidneys and pancreas in a neonate with an HNF1B mutation","authors":"Y. Inaba, R. Hamada, Ryoko Harada, Junya Hashimoto, Wataru Kubota, Chikako Terano, N. Mikami, H. Hataya, Junpei Kuroda, Uiko Mizuguchi, R. Kakinuma, Masatoshi Kondo, T. Kono, M. Honda","doi":"10.3165/jjpn.cr.2020.0175","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2020.0175","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"21 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125906632","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Medical safety management at university hospital","authors":"H. Tsukahara","doi":"10.3165/jjpn.rv.2022.0003","DOIUrl":"https://doi.org/10.3165/jjpn.rv.2022.0003","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"54 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128800685","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
K. Kamei, Mai Sato, Miki Murakoshi, Ryutaro Suzuki, C. Kamae, T. Kanamori, K. Nishi, M. Ogura
{"title":"Relapse of nephrotic syndrome during B-cell depletion after single dose of rituximab","authors":"K. Kamei, Mai Sato, Miki Murakoshi, Ryutaro Suzuki, C. Kamae, T. Kanamori, K. Nishi, M. Ogura","doi":"10.3165/jjpn.oa.2019.0159","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2019.0159","url":null,"abstract":"We investigated the clinical character of relapses of nephrotic syndrome during B-cell depletion in 137 patients with refractory steroid-dependent nephrotic syndrome who received 375 mg/m 2 of single dose of rituximab. In 440 rituximab treatment, relapses during B-cell deletion were observed 25 times in 19 patients (5.7%). Forty-four percent of them were observed within 14 days after treatment of rituximab. Gender, age of onset of nephrotic syndrome, age at rituximab treatment, renal histology, past histories of steroid resistance showed no difference between patients who relapsed during B-cell depletion and others. Infusion reaction also was not calculated as a risk factor. Two third of patients who relapsed during B-cell depletion could discontinue steroid during B-cell depletion, which showed effectiveness of rituximab. According to the result of this study, we believe that we should maintain doses of steroid as relapse-preventable doses until two weeks after rituximab treatment. Even if patients suffered from relapse during B-cell depletion, rituximab might be effective and their disease character might be pathogenetically same as others. As we could not detect risk factors of relapse during B-cell depletion, prediction is difficult.","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129249827","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}