Japanese journal of pediatric nephrology最新文献

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A case of IgA vasculitis, acute glomerulonephritis and Henoch-Schönlein purpura nephritis: successional complications of streptococcal infection IgA血管炎、急性肾小球肾炎和Henoch-Schönlein紫癜性肾炎1例:链球菌感染的连续并发症
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2020.0176
Minamura Takeichi, Mari Kurokawa, Shinichi Shiona, Y. Kaku
{"title":"A case of IgA vasculitis, acute glomerulonephritis and Henoch-Schönlein purpura nephritis: successional complications of streptococcal infection","authors":"Minamura Takeichi, Mari Kurokawa, Shinichi Shiona, Y. Kaku","doi":"10.3165/jjpn.cr.2020.0176","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2020.0176","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115619013","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
母親に体細胞モザイクや生殖細胞系列モザイク変異を有することが疑われたX連鎖型Alport症候群の男児例 被怀疑母亲体内有体细胞马赛克或生殖细胞系列马赛克变异的X连锁性Alport症候群男孩例子
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2022.0215
Kyoko Suzuki, Takuji Yamada
{"title":"母親に体細胞モザイクや生殖細胞系列モザイク変異を有することが疑われたX連鎖型Alport症候群の男児例","authors":"Kyoko Suzuki, Takuji Yamada","doi":"10.3165/jjpn.cr.2022.0215","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2022.0215","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"57 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125127534","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Efficacy and safety of long-term administration of mycophenolate mofetil after rituximab in patients with refractory nephrotic syndrome 难治性肾病综合征患者利妥昔单抗后长期服用霉酚酸酯的疗效和安全性
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.oa.2022.0203
Yooka Nam, R. Hiramoto, S. Shinozuka, S. Matsumoto, H. Eguchi, B. Akikusa
{"title":"Efficacy and safety of long-term administration of mycophenolate mofetil after rituximab in patients with refractory nephrotic syndrome","authors":"Yooka Nam, R. Hiramoto, S. Shinozuka, S. Matsumoto, H. Eguchi, B. Akikusa","doi":"10.3165/jjpn.oa.2022.0203","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2022.0203","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"180 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122520358","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A 3-year-old boy with steroid-resistant nephrotic syndrome who was diagnosed with severe lupus nephritis one year later: a case report 一名患有类固醇抵抗性肾病综合征的三岁男孩,一年后被诊断为严重狼疮肾炎:病例报告
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2021.0202
R. Ohyama, Mayu Nakagawa, T. Morishita, Shota Endo, Y. Takemasa, Yuta Onuki, Koji Sakuraya, H. Murakami, S. Fujinaga
{"title":"A 3-year-old boy with steroid-resistant nephrotic syndrome who was diagnosed with severe lupus nephritis one year later: a case report","authors":"R. Ohyama, Mayu Nakagawa, T. Morishita, Shota Endo, Y. Takemasa, Yuta Onuki, Koji Sakuraya, H. Murakami, S. Fujinaga","doi":"10.3165/jjpn.cr.2021.0202","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2021.0202","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129682011","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Clinical sequencing for nephrologists 肾科医生的临床测序
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.rv.2021.0002
N. Morisada, Kana Hiromoto
{"title":"Clinical sequencing for nephrologists","authors":"N. Morisada, Kana Hiromoto","doi":"10.3165/jjpn.rv.2021.0002","DOIUrl":"https://doi.org/10.3165/jjpn.rv.2021.0002","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133966447","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Assessment of skills in pediatric renal urology procedures among young pediatricians 年轻儿科医生在儿科肾泌尿外科手术中的技能评估
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.oa.2021.0197
Koji Sakuraya, A. Endo, Akina Matsuda, Hiroki Miyano, Hiroaki Gonda, Masahito Saito, Akira Mizutani, Y. Ohtomo
{"title":"Assessment of skills in pediatric renal urology procedures among young pediatricians","authors":"Koji Sakuraya, A. Endo, Akina Matsuda, Hiroki Miyano, Hiroaki Gonda, Masahito Saito, Akira Mizutani, Y. Ohtomo","doi":"10.3165/jjpn.oa.2021.0197","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2021.0197","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"200 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128592421","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Characteristic ultrasonic view of the kidneys and pancreas in a neonate with an HNF1B mutation 新生儿HNF1B突变的肾脏和胰腺的特征性超声图像
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2020.0175
Y. Inaba, R. Hamada, Ryoko Harada, Junya Hashimoto, Wataru Kubota, Chikako Terano, N. Mikami, H. Hataya, Junpei Kuroda, Uiko Mizuguchi, R. Kakinuma, Masatoshi Kondo, T. Kono, M. Honda
{"title":"Characteristic ultrasonic view of the kidneys and pancreas in a neonate with an HNF1B mutation","authors":"Y. Inaba, R. Hamada, Ryoko Harada, Junya Hashimoto, Wataru Kubota, Chikako Terano, N. Mikami, H. Hataya, Junpei Kuroda, Uiko Mizuguchi, R. Kakinuma, Masatoshi Kondo, T. Kono, M. Honda","doi":"10.3165/jjpn.cr.2020.0175","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2020.0175","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"21 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125906632","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Medical safety management at university hospital 高校医院医疗安全管理
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.rv.2022.0003
H. Tsukahara
{"title":"Medical safety management at university hospital","authors":"H. Tsukahara","doi":"10.3165/jjpn.rv.2022.0003","DOIUrl":"https://doi.org/10.3165/jjpn.rv.2022.0003","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"54 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128800685","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Relapse of nephrotic syndrome during B-cell depletion after single dose of rituximab 单剂量利妥昔单抗后b细胞耗竭期间肾病综合征复发
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.oa.2019.0159
K. Kamei, Mai Sato, Miki Murakoshi, Ryutaro Suzuki, C. Kamae, T. Kanamori, K. Nishi, M. Ogura
{"title":"Relapse of nephrotic syndrome during B-cell depletion after single dose of rituximab","authors":"K. Kamei, Mai Sato, Miki Murakoshi, Ryutaro Suzuki, C. Kamae, T. Kanamori, K. Nishi, M. Ogura","doi":"10.3165/jjpn.oa.2019.0159","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2019.0159","url":null,"abstract":"We investigated the clinical character of relapses of nephrotic syndrome during B-cell depletion in 137 patients with refractory steroid-dependent nephrotic syndrome who received 375 mg/m 2 of single dose of rituximab. In 440 rituximab treatment, relapses during B-cell deletion were observed 25 times in 19 patients (5.7%). Forty-four percent of them were observed within 14 days after treatment of rituximab. Gender, age of onset of nephrotic syndrome, age at rituximab treatment, renal histology, past histories of steroid resistance showed no difference between patients who relapsed during B-cell depletion and others. Infusion reaction also was not calculated as a risk factor. Two third of patients who relapsed during B-cell depletion could discontinue steroid during B-cell depletion, which showed effectiveness of rituximab. According to the result of this study, we believe that we should maintain doses of steroid as relapse-preventable doses until two weeks after rituximab treatment. Even if patients suffered from relapse during B-cell depletion, rituximab might be effective and their disease character might be pathogenetically same as others. As we could not detect risk factors of relapse during B-cell depletion, prediction is difficult.","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129249827","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
森田賞 《臨床研究部門》 辻ゆり佳 森田赏《临床研究部门》辻ゆり佳
Japanese journal of pediatric nephrology Pub Date : 1900-01-01 DOI: 10.3165/jjpn.2022.3007
{"title":"森田賞 《臨床研究部門》 辻ゆり佳","authors":"","doi":"10.3165/jjpn.2022.3007","DOIUrl":"https://doi.org/10.3165/jjpn.2022.3007","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"249 ","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"120942533","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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