T. A. Mashkova, A. Maltsev, L. A. Alkilani, L. N. Antakova
{"title":"A BLOCKER OF LEUKOTRIENE RECEPTORS IN THE COMPLEX TREATMENT OF EXUDATIVE OTITIS MEANS IN PATIENTS WITH ALLERGIC RHINITIS","authors":"T. A. Mashkova, A. Maltsev, L. A. Alkilani, L. N. Antakova","doi":"10.17513/SPNO.30814","DOIUrl":"https://doi.org/10.17513/SPNO.30814","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"64 1","pages":"71-71"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"82362299","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"ANALYSIS OF THE RUSSIAN UNIVERSITIES STRATEGY TO RECRUIT FOREIGN STUDENTS","authors":"T. A. Olkhovaya, A. R. Khemraeva, V. Paramonov","doi":"10.17513/SPNO.30802","DOIUrl":"https://doi.org/10.17513/SPNO.30802","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"81 1","pages":"24-24"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"85984220","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
I. F. Fedoseeva, T. Y. Bedareva, T. Vizilo, O. S. Pinevich
{"title":"RARE HEREDITARY DISEASE - MUCOPOLYSACCHARIDOSIS TYPE I, HURLER-SCHEIE SYNDROME: CLINICAL OBSERVATION IN A 2-YEAR-OLD CHILD","authors":"I. F. Fedoseeva, T. Y. Bedareva, T. Vizilo, O. S. Pinevich","doi":"10.17513/SPNO.30779","DOIUrl":"https://doi.org/10.17513/SPNO.30779","url":null,"abstract":"Mucopolysaccharidoses (MPS) are hereditary metabolic disorders from the group of lysosomal storage diseases caused by a deficiency of enzymes involved in the cleavage reactions of glycosaminoglycans. The accumulation of glycosaminoglycans in tissues leads to multi-organ damage. Type I MPS is one of the most common types of MPS. MPS type I, Hurler–Scheie syndrome occurs with a population frequency of 1:40 000 – 1: 100 000 live newborns . The clinical picture is dominated by dysmorphic, neurological, visceral manifestations. The multisystem nature of the lesions determines the need for observation of patients by specialists of different profiles - pediatrician, neurologist, orthopedist, cardiologist, ophthalmologist, audiologist. The article presents a clinical and genetic description and analysis of a case of a rare autosomal recessive neurodegenerative disease mucopolysaccharidosis type I, Hurler-Sheye syndrome, in a 2-year-old girl. Combination of specific features of the phenotype: characteristic changes in facial features, hypertrichosis, skeletal deformities of the type of multiple dysostosis, umbilical hernia, cardiac pathology, ophthalmic pathology (corneal degeneration), neurological disorders (delayed speech development), multisystem lesion, as well as increased urinary excretion of dermatan sulfate, a decrease in the activity of alpha-iduronidase in the blood was the basis for the diagnosis: mucopolysaccharidosis type I, Hurler–Scheie syndrome. The diagnosis was confirmed by the results of molecular genetic analysis.","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"29 1","pages":"24-24"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"88950191","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"CREATIVE ACTIVITY AS A PROBLEM FIELD OF RESEARCH","authors":"V. Gorovaya, E. N. Belozubova","doi":"10.17513/SPNO.30872","DOIUrl":"https://doi.org/10.17513/SPNO.30872","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"11 1","pages":"132-132"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"91538762","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"FEATURES OF COMPREHENSIVE TRANSFUSIOLOGICAL SUPPORT IN PATIENTS WITH MASSIVE OBSTETRIC BLEEDING WITH INITIAL ANEMIA","authors":"A. V. Kuligin, A. Lushnikov, E. E. Zeulina","doi":"10.17513/SPNO.30559","DOIUrl":"https://doi.org/10.17513/SPNO.30559","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"47 1","pages":"42-42"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"88834315","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Kiblitskaya, A. N. Shevchenko, O. V. Pandova, A. Ardzha
{"title":"BIOBANKING OF PATIENT-DERIVED XENOGRAFTS AS A BASIS FOR TRANSLATION RESEARCH IN ONCOLOGY","authors":"A. Kiblitskaya, A. N. Shevchenko, O. V. Pandova, A. Ardzha","doi":"10.17513/SPNO.30879","DOIUrl":"https://doi.org/10.17513/SPNO.30879","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"70 1","pages":"127-127"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"85074505","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
N. Agranovich, O. Agranovich, A. Anopchenko, T. Derevyanko, S. A. Knyshova
{"title":"IMPLEMENTATION OF ADDITIONAL PROFESSIONAL EDUCATION AT A MEDICAL UNIVERSITY DURING THE COVID-19 PANDEMIC","authors":"N. Agranovich, O. Agranovich, A. Anopchenko, T. Derevyanko, S. A. Knyshova","doi":"10.17513/SPNO.30600","DOIUrl":"https://doi.org/10.17513/SPNO.30600","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"16 1","pages":"26-26"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"87705531","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"VISUALISATION OF PORONATION-SUPINATION MOVEMENT OF THE FOREARM AS A KEY TO UNDERSTANING THE ROTATIONAL MOBILITY OF THE ULNA IN THE DISTAL RADIOULNAR JOINT","authors":"Y. N. Proschenko, S. Semenov, Y. A. Sigareva","doi":"10.17513/SPNO.30526","DOIUrl":"https://doi.org/10.17513/SPNO.30526","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"1 1","pages":"67-67"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"83533180","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
L. Mosina, E. Y. Surokova, A. Geraskin, E. I. Polozova
{"title":"PATHOGENETIC MECHANISMS OF DIRECT AND SECONDARY INTESTINAL LESION IN PATIENTS WITH CORONARVIRAL INFECTION CAUSED BY THE SARS-COV-2 VIRUS","authors":"L. Mosina, E. Y. Surokova, A. Geraskin, E. I. Polozova","doi":"10.17513/SPNO.30754","DOIUrl":"https://doi.org/10.17513/SPNO.30754","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"20 15","pages":"203-203"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"91418568","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"ADDITIONAL DISTANCE MEDICAL EDUCATION: A MODERN VIEW IN THE CONDITIONS OF THE COVID-19 PANDEMIC","authors":"A. Maltseva, V. Maltsev, L. S. Maltseva","doi":"10.17513/SPNO.30778","DOIUrl":"https://doi.org/10.17513/SPNO.30778","url":null,"abstract":"","PeriodicalId":18624,"journal":{"name":"Modern Problems of Science and Education","volume":"625 1","pages":"12-12"},"PeriodicalIF":0.0,"publicationDate":"2021-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"77620192","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}