C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)最新文献

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Polysomnography Findings in Children's Interstitial Lung Disease (chILD) 儿童间质性肺疾病(儿童)的多导睡眠图表现
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5471
R. Inja, K. Garagozlo, K. Graw-Panzer, G. Loughlin
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引用次数: 0
Interstitial Lung Disease in a Patient Heterozygous for Two Previously Undescribed VUS in SFPTC SFPTC中两种先前未描述的VUS的杂合性肺间质性疾病
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474
S. Karandashova, N. Ly
{"title":"Interstitial Lung Disease in a Patient Heterozygous for Two Previously Undescribed VUS in SFPTC","authors":"S. Karandashova, N. Ly","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116311977","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A Rare Case of Interstitial Lung Disease and Pulmonary Hypertension Associated With NKX2-1 Mutation 罕见的间质性肺疾病和肺动脉高压与NKX2-1突变有关
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476
J. Ni, J. Cameron, R. Hopper, S. Tan, X. Si
{"title":"A Rare Case of Interstitial Lung Disease and Pulmonary Hypertension Associated With NKX2-1 Mutation","authors":"J. Ni, J. Cameron, R. Hopper, S. Tan, X. Si","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115265418","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A Rare Pediatric Case of Anti-melanoma Differentiation-associated Gene 5 Rapidly Progressive Interstitial Lung Disease 罕见的儿童抗黑色素瘤分化相关基因5快速进展间质性肺病病例
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5475
K. Gallagher, R. Ortenberg, D. Toprak
{"title":"A Rare Pediatric Case of Anti-melanoma Differentiation-associated Gene 5 Rapidly Progressive Interstitial Lung Disease","authors":"K. Gallagher, R. Ortenberg, D. Toprak","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5475","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5475","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131384165","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Pulmonary Hemorrhage and Massive Air-leak: An Atypical Presentation for Pulmonary Interstitial Glycogenosis 肺出血和大量漏气:肺间质性糖原症的不典型表现
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477
L. A. García Bonilla, J. Chiang
{"title":"Pulmonary Hemorrhage and Massive Air-leak: An Atypical Presentation for Pulmonary Interstitial Glycogenosis","authors":"L. A. García Bonilla, J. Chiang","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123703720","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
An Additional ABCA3 Mutation May Worsen SFTPC Associated Childhood Interstitial Lung Disease. 一个额外的ABCA3突变可能加重SFTPC相关的儿童间质性肺疾病。
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5473
S. Karandashova, M. Chan, A. Shum, N. Ly
{"title":"An Additional ABCA3 Mutation May Worsen SFTPC Associated Childhood Interstitial Lung Disease.","authors":"S. Karandashova, M. Chan, A. Shum, N. Ly","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5473","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5473","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131132992","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Low Serum Progranulin Levels as a Biomarker in the First Reported Case of Progranulin (GRN) Variant Associated Fibrotic Lung and Liver Disease 低血清前颗粒蛋白水平作为首个报道的前颗粒蛋白(GRN)变异相关纤维化肺和肝脏疾病的生物标志物
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481
J. Kennedy, S. Vargas, M. Fishman, C. Garcia de Alba Rivas, S. Baek, N. Alesi, N. Carmichael, A. Casey, D. Khabibullin, L. Henderson, A. Wehrman, L. Collen, B. Raby
{"title":"Low Serum Progranulin Levels as a Biomarker in the First Reported Case of Progranulin (GRN) Variant Associated Fibrotic Lung and Liver Disease","authors":"J. Kennedy, S. Vargas, M. Fishman, C. Garcia de Alba Rivas, S. Baek, N. Alesi, N. Carmichael, A. Casey, D. Khabibullin, L. Henderson, A. Wehrman, L. Collen, B. Raby","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122549191","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Healthcare Utilization in Childhood Interstitial Lung Disease: A Report From a Major Tertiary Care Center 儿童间质性肺病的医疗保健利用:一份来自主要三级保健中心的报告
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467
L. Feld, Z. Li, M. Josephson, J. Rice, D. Camburn, Y. Li, S. McGrath-Morrow, L. Young
{"title":"Healthcare Utilization in Childhood Interstitial Lung Disease: A Report From a Major Tertiary Care Center","authors":"L. Feld, Z. Li, M. Josephson, J. Rice, D. Camburn, Y. Li, S. McGrath-Morrow, L. Young","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133633168","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Miliary Pattern Chest Imaging Presentation of COPA Syndrome in a Pediatric Patient 小儿COPA综合征的军型胸部影像学表现
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479
C. Mertens, G. B. Beltran Ale
{"title":"Miliary Pattern Chest Imaging Presentation of COPA Syndrome in a Pediatric Patient","authors":"C. Mertens, G. B. Beltran Ale","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131255041","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Estimating the Effect of Nintedanib on Forced Vital Capacity in Children and Adolescents With Fibrosing Interstitial Lung Disease: Extrapolation Using a Bayesian Borrowing Approach 估计尼达尼布对患有纤维化间质性肺疾病的儿童和青少年强制肺活量的影响:使用贝叶斯借用方法的外推
C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD) Pub Date : 2023-05-01 DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465
T. M. Maher, K. Brown, S. Cunningham, E. DeBoer, R. Deterding, E. Fiorino, M. Griese, N. Schwerk, D. Warburton, L. Young, M. Gahlemann, F. Voß, C. Stock, on behalf of the InPedILD trial investigators
{"title":"Estimating the Effect of Nintedanib on Forced Vital Capacity in Children and Adolescents With Fibrosing Interstitial Lung Disease: Extrapolation Using a Bayesian Borrowing Approach","authors":"T. M. Maher, K. Brown, S. Cunningham, E. DeBoer, R. Deterding, E. Fiorino, M. Griese, N. Schwerk, D. Warburton, L. Young, M. Gahlemann, F. Voß, C. Stock, on behalf of the InPedILD trial investigators","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115938399","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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