{"title":"Interstitial Lung Disease in a Patient Heterozygous for Two Previously Undescribed VUS in SFPTC","authors":"S. Karandashova, N. Ly","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"82 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116311977","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A Rare Case of Interstitial Lung Disease and Pulmonary Hypertension Associated With NKX2-1 Mutation","authors":"J. Ni, J. Cameron, R. Hopper, S. Tan, X. Si","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115265418","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Pulmonary Hemorrhage and Massive Air-leak: An Atypical Presentation for Pulmonary Interstitial Glycogenosis","authors":"L. A. García Bonilla, J. Chiang","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"19 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123703720","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
J. Kennedy, S. Vargas, M. Fishman, C. Garcia de Alba Rivas, S. Baek, N. Alesi, N. Carmichael, A. Casey, D. Khabibullin, L. Henderson, A. Wehrman, L. Collen, B. Raby
{"title":"Low Serum Progranulin Levels as a Biomarker in the First Reported Case of Progranulin (GRN) Variant Associated Fibrotic Lung and Liver Disease","authors":"J. Kennedy, S. Vargas, M. Fishman, C. Garcia de Alba Rivas, S. Baek, N. Alesi, N. Carmichael, A. Casey, D. Khabibullin, L. Henderson, A. Wehrman, L. Collen, B. Raby","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"104 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122549191","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Miliary Pattern Chest Imaging Presentation of COPA Syndrome in a Pediatric Patient","authors":"C. Mertens, G. B. Beltran Ale","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131255041","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
L. Feld, Z. Li, M. Josephson, J. Rice, D. Camburn, Y. Li, S. McGrath-Morrow, L. Young
{"title":"Healthcare Utilization in Childhood Interstitial Lung Disease: A Report From a Major Tertiary Care Center","authors":"L. Feld, Z. Li, M. Josephson, J. Rice, D. Camburn, Y. Li, S. McGrath-Morrow, L. Young","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"129 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133633168","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
T. M. Maher, K. Brown, S. Cunningham, E. DeBoer, R. Deterding, E. Fiorino, M. Griese, N. Schwerk, D. Warburton, L. Young, M. Gahlemann, F. Voß, C. Stock, on behalf of the InPedILD trial investigators
{"title":"Estimating the Effect of Nintedanib on Forced Vital Capacity in Children and Adolescents With Fibrosing Interstitial Lung Disease: Extrapolation Using a Bayesian Borrowing Approach","authors":"T. M. Maher, K. Brown, S. Cunningham, E. DeBoer, R. Deterding, E. Fiorino, M. Griese, N. Schwerk, D. Warburton, L. Young, M. Gahlemann, F. Voß, C. Stock, on behalf of the InPedILD trial investigators","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"40 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115938399","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}