Pushkar Sharma, P. Jacob, Santosh Raj, E. Sigamani, M. Manipadam
{"title":"Composite Pheochromocytoma—A Rare Clinical Entity: A Case Series","authors":"Pushkar Sharma, P. Jacob, Santosh Raj, E. Sigamani, M. Manipadam","doi":"10.5005/jp-journals-10088-11151","DOIUrl":"https://doi.org/10.5005/jp-journals-10088-11151","url":null,"abstract":"Background: Composite pheochromocytoma is a rare entity with tumor comprising both pheochromocytoma and neuroblastic elements. The clinical outcome of such a composite tumor is not fully understood. In this case series, we report three cases of composite pheochromocytoma managed at our institute from 2016 to 2021. Results: We had three patients with MEN2A syndrome with composite tumor who underwent adrenalectomy, all of which were ganglioneuroma with pheochromocytoma. None of the three cases had recurrence or metastasis associated with composite adrenal tumor on 13-month mean follow-up. Conclusion: We noticed a higher incidence of syndromic association in composite adrenal tumors. The clinical and radiological presentation was dominated by the pheochromocytoma component.","PeriodicalId":135260,"journal":{"name":"Indian Journal of Endocrine Surgery and Research","volume":"20 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-08-26","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116179575","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
G. Bhat, P. Ramakant, L. Enny, Surabhi Garg, Kulranjan Singh, Anshuman Mishra
{"title":"Challenges for the Endocrine Surgeon in the Decision-making in Managing Head and Neck Paragangliomas","authors":"G. Bhat, P. Ramakant, L. Enny, Surabhi Garg, Kulranjan Singh, Anshuman Mishra","doi":"10.5005/jp-journals-10088-11153","DOIUrl":"https://doi.org/10.5005/jp-journals-10088-11153","url":null,"abstract":"Head and neck paraganglioma tumors present with a lot of challenges in decision-making for choosing the most appropriate management option for particular patients. We present a young patient who is a 22-year-old lady with neck mass for 7 years duration with a gradual increase. There was a significant family history of a sister dying at 18 years of age due to an unknown cause. She was normotensive, nonfunctional, and had a large neck mass reaching up to the base of the skull. As it was considered inoperable, we explored other treatment options and gave her radiation therapy. The tumor mass reduced 60% in 8 months duration. We have kept her in close follow-up with repeat imaging at 6 months intervals. Conclusion: We need to a tailor-made treatment option for each patient with neck paraganglioma and chose wisely among surgery with or without preoperative embolization and radiation therapy.","PeriodicalId":135260,"journal":{"name":"Indian Journal of Endocrine Surgery and Research","volume":"62 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-08-26","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115984301","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}