TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE最新文献

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"Fatty Lungs": A Uncommon Case of Autoimmune Pulmonary Alveolar Proteinosis “脂肪肺”:一个罕见的自身免疫性肺泡蛋白沉积症病例
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 2021-08-05 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2051
A. Nieves-Ortiz, K. Hernandez-Moya, Juan Garcia-Puebla, Kimberly Padilla-Rodriguez, N. Roman-Velez, Giovanni Veloz-Irizarry, K. Mendez-Ramirez, H. Collazo-Santiago, José Adorno-Fontánez, Ricardo Fernández-González
{"title":"\"Fatty Lungs\": A Uncommon Case of Autoimmune Pulmonary Alveolar Proteinosis","authors":"A. Nieves-Ortiz, K. Hernandez-Moya, Juan Garcia-Puebla, Kimberly Padilla-Rodriguez, N. Roman-Velez, Giovanni Veloz-Irizarry, K. Mendez-Ramirez, H. Collazo-Santiago, José Adorno-Fontánez, Ricardo Fernández-González","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2051","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2051","url":null,"abstract":"Pulmonary Alveolar Proteinosis (PAP) is a rare lung disease characterized by excessive accumulation of surfactant lipids and proteins in alveoli and terminal airways. It is caused by impaired GM-CSF signaling [1]. Surfactant is synthesized and secreted by alveolar type II epithelial cells, and removed by uptake and catabolism by these cells, and the alveolar macrophages. Patients with PAP usually describe gradual onset of progressive exertional dyspnea and non-productive cough. However, an asymptomatic presentation is observed in up to 25% of cases, even in the presence of diffuse radiographic changes. Three recognized subtypes exist. Autoimmune PAP is associated with neutralizing GM-CSF autoantibodies and accounts about 90% of cases. Secondary PAP may occur in the context of any disease that reduces the abundance or functionality of alveolar macrophages, resulting in impaired surfactant clearance. Congenital PAP is the result of genetic mutations that disrupt GM-CSF signaling, including mutations in the αor β-chains of the GM-CSF receptor [1-3].","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"20 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-08-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124628699","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Granulomatosis with Polyangiitis with Peripheral Eosinophilia and Diffuse Alveolar Hemorrhage 肉芽肿病伴多血管炎伴外周血嗜酸性粒细胞增多和弥漫性肺泡出血
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2043
N. Haris, A. Ladzinski, J. Brooks, P. Patel
{"title":"Granulomatosis with Polyangiitis with Peripheral Eosinophilia and Diffuse Alveolar Hemorrhage","authors":"N. Haris, A. Ladzinski, J. Brooks, P. Patel","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2043","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2043","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"31 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114457871","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
White-Out Lungs: A Case of Autoimmune Pulmonary Alveolar Proteinosis 自身免疫性肺泡蛋白沉积症1例
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2052
D. Kazmierski, N. Sharma, B. Noumi, M. Amjad, P. Ochieng
{"title":"White-Out Lungs: A Case of Autoimmune Pulmonary Alveolar Proteinosis","authors":"D. Kazmierski, N. Sharma, B. Noumi, M. Amjad, P. Ochieng","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2052","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2052","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"29 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130197283","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Association of Interstitial Lung Disease and Pneumomediastine in Idiopathic inflammatory Myopathy 特发性炎性肌病间质性肺病与纵隔气肿的关系
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2067
S. San Martín, G.D.P. Bridi, G. Almeida, P. Colares, R. Kairalla
{"title":"Association of Interstitial Lung Disease and Pneumomediastine in Idiopathic inflammatory Myopathy","authors":"S. San Martín, G.D.P. Bridi, G. Almeida, P. Colares, R. Kairalla","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2067","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2067","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"243 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128880867","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A Case of Progressive Interstitial Lung Disease in a 25-Year-Old Woman, 34 Weeks Pregnant, Who Presents with Cough and Fever 进行性间质性肺病1例,25岁女性,怀孕34周,表现为咳嗽和发烧
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2063
E. Kistler, L. Hariri, K. Berg
{"title":"A Case of Progressive Interstitial Lung Disease in a 25-Year-Old Woman, 34 Weeks Pregnant, Who Presents with Cough and Fever","authors":"E. Kistler, L. Hariri, K. Berg","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2063","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2063","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"73 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125761056","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Adult Patient with Pulmonary Hemosiderosis and Celiac Disease (Lane Hamilton Syndrome): A Case Report 成人肺含铁血黄素沉着合并乳糜泻(Lane Hamilton综合征)1例报告
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2047
N. Zimmermann, P. Colares, I. Holz, A. F. Amaral, A. M. Kawassaki, B. Baldi, R. Kairalla
{"title":"Adult Patient with Pulmonary Hemosiderosis and Celiac Disease (Lane Hamilton Syndrome): A Case Report","authors":"N. Zimmermann, P. Colares, I. Holz, A. F. Amaral, A. M. Kawassaki, B. Baldi, R. Kairalla","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2047","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2047","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129885423","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Immunoglobulin G4-Related Disease (IgG4-RD) - An Unusual Presentation Mimicking Metastatic Lung Cancer. 免疫球蛋白g4相关疾病(IgG4-RD) -一种模拟转移性肺癌的不寻常表现
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2056
R. Kunadharaju, D. Crossland, B. Ahmed, A. Saradna, M. Mador
{"title":"Immunoglobulin G4-Related Disease (IgG4-RD) - An Unusual Presentation Mimicking Metastatic Lung Cancer.","authors":"R. Kunadharaju, D. Crossland, B. Ahmed, A. Saradna, M. Mador","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2056","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2056","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"29 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130507869","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A Case of Anti-Glomerular Basement Membrane Disease Presented with Pulmonary Renal Syndrome Treated with Rituximab 抗肾小球基底膜病合并肺肾综合征1例利妥昔单抗治疗
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2041
S. Shrestha, P. Mckillion, A. Abdullah, S. Penupolu
{"title":"A Case of Anti-Glomerular Basement Membrane Disease Presented with Pulmonary Renal Syndrome Treated with Rituximab","authors":"S. Shrestha, P. Mckillion, A. Abdullah, S. Penupolu","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2041","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2041","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"7 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131657708","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
An Unusual Presentation of New Systemic Lupus Erythematous: Concomitant Methicillin-Susceptible Staphylococcus Aureus Bacteremia and Severe Hyponatremia 新的系统性红斑狼疮的不寻常表现:伴随甲氧西林敏感金黄色葡萄球菌菌血症和严重低钠血症
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2034
J. Bae, K. Hsieh, K. Bortfeld, S. D’Annunzio
{"title":"An Unusual Presentation of New Systemic Lupus Erythematous: Concomitant Methicillin-Susceptible Staphylococcus Aureus Bacteremia and Severe Hyponatremia","authors":"J. Bae, K. Hsieh, K. Bortfeld, S. D’Annunzio","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2034","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2034","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126795186","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Misdiagnosis of Asthma in a Patient with Hypereosinophilic Syndrome with Cardiac Involvement 高嗜酸性粒细胞综合征伴心脏受累患者哮喘的误诊
TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE Pub Date : 1900-01-01 DOI: 10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2031
M. Riego, J. Poon, R. Naik
{"title":"Misdiagnosis of Asthma in a Patient with Hypereosinophilic Syndrome with Cardiac Involvement","authors":"M. Riego, J. Poon, R. Naik","doi":"10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2031","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2021.203.1_meetingabstracts.a2031","url":null,"abstract":"","PeriodicalId":114116,"journal":{"name":"TP33. TP033 CASE REPORTS IN AUTOIMMUNE LUNG DISEASE","volume":"101 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122963059","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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