Cardiologie tunisienne最新文献

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[Circular shunt in the severe neonatal form of Ebstein's Anomaly. The prostaglandine infusion is it beneficial or harmful?] [圆形分流术在新生儿重度Ebstein异常中的应用]前列腺素输注是有益还是有害?］

Cardiologie tunisienne Pub Date : 2013-10-01

Kaouthar Hakim, Rafik Boussaada, Jihen Ayari, Hamdi Imen, Hela Msaad, Fatma Ouarda, Lilia Chaker

{"title":"[Circular shunt in the severe neonatal form of Ebstein's Anomaly. The prostaglandine infusion is it beneficial or harmful?]","authors":"Kaouthar Hakim, Rafik Boussaada, Jihen Ayari, Hamdi Imen, Hela Msaad, Fatma Ouarda, Lilia Chaker","doi":"","DOIUrl":"","url":null,"abstract":"Ebstein's disease with functional pulmonary atresia is a severe neonatal presentation of Ebstein's anomaly where the therapeutic management is typically based on the prescription of prostaglandins. The circular shunt is a serious \"hemodynamic\" complication which is often undiagnosed leading to the discontinuation of prostaglandins. We report a severe neonatal form of Ebstein's anomaly with hemodynamic deterioration relatted to a circular shunt. The diagnosis of Ebstein's anomaly with functional pulmonary atresia was made prenatally at 36 weeks of pregnancy. The patient was born at 38 weeks of gestation by caesarean section. Postnatal ultrasound confirmed the diagnosis. Treatment with prostaglandins was originally created to maintain the vital ductus arteriosus patent. Despite this treatment, hemodynamic deterioration was observed. Ultrasound monitoring showed pictures for a circular shunt. Indeed, blood coming into the pulmonary artery by the wide ductus arteriosus, was \"drawn\" to the right ventricle and the right atrium due to tricuspid regurgitation and from there to the left heart via the fossa ovalis shunting right to left, when it was ejected into the aorta and the ductus arteriosus. Before this circular shunt, treatment with prostaglandin was discontinued and treatment to reduce pulmonary resistance was described. However, the patient died prior to initiation of treatment. The neonatal form of Ebstein's anomaly is a severe form that can be complicated by a circular shunt. This hemodynamic phenomenon encourages early closure of the ductus arteriosus against indicating the prescription of prostaglandins.","PeriodicalId":90462,"journal":{"name":"Cardiologie tunisienne","volume":"9 4","pages":"73-76"},"PeriodicalIF":0.0,"publicationDate":"2013-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4311569/pdf/nihms624873.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"33020900","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Giant aortic arch aneurysm complicating Kawasaki disease: an original case report. 巨主动脉弓动脉瘤合并川崎病1例报告。

Cardiologie tunisienne Pub Date : 2013-01-01

Hakim Kaouthar, Boussaada Rafik, Ayari Jihen, Hamdi Imen, Chaker Lilia, Ouarda Fatma, Msaad Hela

引用次数: 0

Cardiac anomalies in Cantrell's pentalogy: From ventricular diverticulum to complete thoracic ectopia cordis. Cantrell五联症的心脏异常:从心室憩室到完全性胸椎异位。

Cardiologie tunisienne Pub Date : 2013-01-01

Hakim Kaouthar, Ayari Jihen, Jebri Faten, Msaad Hela, Ouarda Fatma, Chaker Lilia, Boussaada Rafik

{"title":"Cardiac anomalies in Cantrell's pentalogy: From ventricular diverticulum to complete thoracic ectopia cordis.","authors":"Hakim Kaouthar, Ayari Jihen, Jebri Faten, Msaad Hela, Ouarda Fatma, Chaker Lilia, Boussaada Rafik","doi":"","DOIUrl":"","url":null,"abstract":"Cantrell's pentalogy is a very rare syndrome associating varying degrees of midline wall defects and congenital cardiac anomalies. It is characterized by a combination of five anomalies that are: a midline supra umbilical abdominal wall defect, a sternal defect, an anterior diaphragmatic defect, a diaphragmatic pericardial defect and a congenital intra cardiac defect. Ectopia cordis, defined as a developmental defect in which the heart is abnormally located partially or totally outside the thorax, is in some cases a part of this syndrome. We report two cases of Cantrell's pentalogy in which cardiac ectopia was complete in one case and limited to left ventricular diverticulum in the other case. Both cases had a common intracardiac defect which is a double outlet right ventricle. The first case underwent surgical repair of the intracardiac lesions with resection of the diverticulum associated to repair of the midline defects with good outcome. The second case that presented with complete extra thoracic ectopia cordis died because of sepsis. We review through this article the main characteristics of Cantrell's pentalogy, we highlight the diversity of anatomic lesions and study the prognosis of this syndrome.","PeriodicalId":90462,"journal":{"name":"Cardiologie tunisienne","volume":"9 1","pages":"94-97"},"PeriodicalIF":0.0,"publicationDate":"2013-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4274934/pdf/nihms-624965.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"32935342","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0