Moyamoya Disease [Working Title]最新文献

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Moyamoya Disease Worldwide-Global Burden East and West 全球烟雾病-东西方的全球负担

Moyamoya Disease [Working Title] Pub Date : 2021-03-04 DOI: 10.5772/INTECHOPEN.96137

M. Mehndiratta, Ishu Goyal, Vasundhara Aggarwal, N. Gulati

{"title":"Moyamoya Disease Worldwide-Global Burden East and West","authors":"M. Mehndiratta, Ishu Goyal, Vasundhara Aggarwal, N. Gulati","doi":"10.5772/INTECHOPEN.96137","DOIUrl":"https://doi.org/10.5772/INTECHOPEN.96137","url":null,"abstract":"The Moyamoya disease [MMD] is a cereberovascular disorder characterized by progressive stenosis of intracranial internal carotid arteries and compensatory collateral formation at the base of the brain, mainly around the circle of Willis. When no particular associated risk factors can be identified, it is termed as Moyamoya disease. However, it may be associated with other neurological and extra- neurological disorders where it is termed as Moyamoya syndrome [MMS]. The condition is predominantly seen in East Asia and has bimodal age of distribution. The clinical manifestations are also age dependant with ischemia predominating in childhood and hemorrhagic manifestations being more common in adults. The pathogenesis is not entirely known, but genetic susceptibility is believed to be an important predisposing factor. The Suzuki staging system is most widely used for evaluation and staging of Moyamoya disease. The gold standard diagnostic modality is cerebral angiography but magnetic resonance imaging [MRA] has also been employed for diagnosis. Treatment is primarily surgical revascularization which is of 3 types: direct, indirect or combined revascularization. Although the role of revascularization surgery has been well established for ischemic MMD, the ideal surgical approach and the role of surgery in hemorrhagic MMD remains controversial.","PeriodicalId":231669,"journal":{"name":"Moyamoya Disease [Working Title]","volume":"43 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-03-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122625815","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Perioperative Considerations for Revascularization and Non-Revascularization Surgeries in Moyamoya Disease 烟雾病血运重建术与非血运重建术围手术期的考虑

Moyamoya Disease [Working Title] Pub Date : 2021-03-02 DOI: 10.5772/INTECHOPEN.96564

Muhammad Jaffar Khan, Jazib Hassan, S. Aboobacker, Tarek A Tageldin, J. faraj, M. Elarref

{"title":"Perioperative Considerations for Revascularization and Non-Revascularization Surgeries in Moyamoya Disease","authors":"Muhammad Jaffar Khan, Jazib Hassan, S. Aboobacker, Tarek A Tageldin, J. faraj, M. Elarref","doi":"10.5772/INTECHOPEN.96564","DOIUrl":"https://doi.org/10.5772/INTECHOPEN.96564","url":null,"abstract":"Moyamoya disease is a rare, progressive cerebrovascular occlusive disease; characterized by narrowing of the distal internal carotid arteries and their branches. The incidence is high in East Asians and most commonly presents in the first and fourth decade of life. Its symptoms are headaches, seizures, transient neurological deficits, and cognitive decline. Medical management is based on treating the symptoms and includes antiplatelet and anti-seizure medications. Surgical revascularization is the mainstay of treatment. Unique pathophysiology of moyamoya disease necessitates neuro-anesthesiologists to formulate an individualized plan perioperatively. The overriding goal of perioperative anesthetic management of moyamoya disease is to ensure optimal cerebral perfusion and protection. Maintenance of normotension, normocarbia, normo-oxygenation, normothermia, and euvolemia is the cornerstone during the perioperative period. Perioperative adequate analgesia is crucial to prevent cerebral ischemia and allows close neurological monitoring. This chapter reviews perioperative anesthetic management of patients with moyamoya disease.","PeriodicalId":231669,"journal":{"name":"Moyamoya Disease [Working Title]","volume":"136 ","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-03-02","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"113992269","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Medical Management in Moyamoya Disease 烟雾病的医疗管理

Moyamoya Disease [Working Title] Pub Date : 2021-01-30 DOI: 10.5772/INTECHOPEN.95775

N. Uransilp, Sirinat Puengcharoen, S. Muengtaweepongsa

引用次数: 1