大疱性表皮松解症患者适应家庭夜间血液透析:呼唤个性化护理!

IF 16.4 1区化学 Q1 CHEMISTRY, MULTIDISCIPLINARY

Accounts of Chemical Research Pub Date : 2023-04-13 DOI:10.1111/hdi.13086

Rose Faratro, Christopher T. Chan

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引用次数: 0

摘要

大疱性表皮松解症(EB)是一种遗传性疾病，以皮肤脆弱为特征，表现为起泡和皮肤糜烂。反复皮肤感染被认为与IgA肾病的发病机制有关。终末期肾病(ESKD)是EB患者中一种罕见的并发症(Ducret F.等，Nephrol Ther, 2008)。肾脏替代疗法在这一弱势患者群体中非常具有挑战性(Fine JD。et al.， Am J Kidney Dis, 2004)。在此，我们描述了适应我们的家庭夜间血液透析培训和操作，以促进EB和ESKD患者接受个性化的家庭夜间血液透析治疗。

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Adaptation of home nocturnal hemodialysis for a patient with epidermolysis bullosa: A call to personalized care!

Epidermolysis bullosa (EB) is a genetic disease characterized by skin fragility presenting with blistering and skin erosions. Recurrent skin infections are noted to be associated with the pathogenesis of IgA nephropathy. End stage kidney disease (ESKD) is a rare complication in patients with EB (Ducret F., et al., Nephrol Ther, 2008). Kidney replacement therapy is very challenging in this vulnerable patient population (Fine JD. et al., Am J Kidney Dis, 2004). Herein, we describe the adaptations to our home nocturnal hemodialysis training and operations to facilitate a patient with EB and ESKD to undergo personalized home nocturnal hemodialysis therapy.

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来源期刊

Accounts of Chemical Research 化学-化学综合

CiteScore

31.40

自引率

1.10%

发文量

312

审稿时长

2 months

期刊介绍： Accounts of Chemical Research presents short, concise and critical articles offering easy-to-read overviews of basic research and applications in all areas of chemistry and biochemistry. These short reviews focus on research from the author’s own laboratory and are designed to teach the reader about a research project. In addition, Accounts of Chemical Research publishes commentaries that give an informed opinion on a current research problem. Special Issues online are devoted to a single topic of unusual activity and significance. Accounts of Chemical Research replaces the traditional article abstract with an article "Conspectus." These entries synopsize the research affording the reader a closer look at the content and significance of an article. Through this provision of a more detailed description of the article contents, the Conspectus enhances the article's discoverability by search engines and the exposure for the research.