血浆置换治疗暴发性威尔逊病可改善精神状态和凝血功能。

Quarshie Glover, William Nicholas Rose
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引用次数: 0

摘要

威尔逊氏病是一种罕见的遗传病,影响铜代谢,导致组织铜积累和器官损伤。我们报告一例年轻女性威尔逊氏病合并溶血,肝功能受损,凝血功能障碍和急性肾损伤。她接受了血浆置换治疗,作为肝移植的桥梁。血浆置换后患者精神状态、肾功能及胆红素水平均有改善。她成功地接受了肝移植,并在肝移植后保持稳定。我们分享血浆置换治疗肝豆状核变性的经验。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

Plasmapheresis for Fulminant Wilson's Disease Improves Mental Status and Coagulopathy.

Plasmapheresis for Fulminant Wilson's Disease Improves Mental Status and Coagulopathy.

Wilson's disease is a rare genetic condition that affects copper metabolism, resulting in tissue copper accumulation and resultant organ damage. We report a case of a young woman who presents with Wilson's disease complicated by hemolysis, impaired hepatic function, coagulopathy, and acute kidney injury. She was treated with plasmapheresis as a bridge to a liver transplant. Her mental state, renal function, and bilirubin level improved after starting plasmapheresis. She successfully underwent a liver transplant and remained stable post-liver transplant. We share our experience on the use of plasmapheresis in treating Wilson's disease.

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