子宫硬化性血管周类上皮细胞瘤:一种罕见的实体,诊断上有挑战。

IF 1.2 Q3 OBSTETRICS & GYNECOLOGY
Journal of Mid-life Health Pub Date : 2022-10-01 Epub Date: 2023-04-28 DOI:10.4103/jmh.jmh_120_22
Reetu Kundu, Pradip Kumar Saha, Pranab Dey
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引用次数: 0

摘要

血管周围上皮样细胞瘤(PEComa)是一种罕见的子宫间充质肿瘤,其组织学变异、硬化性PEComa极为罕见。硬化性PEComas优先发生在腹膜后,很少发生在子宫体。这些肿瘤对诊断提出了挑战,需要与上皮样平滑肌肿瘤、子宫内膜间质肉瘤和转移癌等形态模拟物区分开来。结合组织形态学和免疫染色可以建立准确的诊断。考虑到治疗和预后影响,与其他实体的区别至关重要。在此,我们描述了一例PEComa的子宫硬化性变体,其诊断困难和诊断该实体的关键。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

Sclerosing Perivascular Epithelioid Cell Tumor of the Uterus: A Rare Entity Posing Diagnostic Challenge.

Sclerosing Perivascular Epithelioid Cell Tumor of the Uterus: A Rare Entity Posing Diagnostic Challenge.

Sclerosing Perivascular Epithelioid Cell Tumor of the Uterus: A Rare Entity Posing Diagnostic Challenge.

Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal uterine tumor and the histological variant, sclerosing PEComa is exceedingly rare. Sclerosing PEComas preferentially occur in the retroperitoneum and occurrence in the uterine corpus is seldom seen. These tumors pose a diagnostic challenge and need distinction from morphological mimickers such as epithelioid smooth muscle tumors, endometrial stromal sarcoma, and metastatic carcinoma. Accurate diagnosis can be established coupling histomorphology with immunostaining. The distinction from other entities is of prime importance considering the therapeutic and prognostic implications. Herein, we describe a case of uterine sclerosing variant of PEComa with diagnostic difficulties and key to diagnose this entity.

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来源期刊
Journal of Mid-life Health
Journal of Mid-life Health Social Sciences-Health (social science)
CiteScore
1.70
自引率
9.10%
发文量
39
审稿时长
43 weeks
期刊介绍: Journal of mid-life health is the official journal of the Indian Menopause society published Quarterly in January, April, July and October. It is peer reviewed, scientific journal of mid-life health and its problems. It includes all aspects of mid-life health, preventive as well as curative. The journal publishes on subjects such as gynecology, neurology, geriatrics, psychiatry, endocrinology, urology, andrology, psychology, healthy ageing, cardiovascular health, bone health, quality of life etc. as relevant of men and women in their midlife. The Journal provides a visible platform to the researchers as well as clinicians to publish their experiences in this area thereby helping in the promotion of mid-life health leading to healthy ageing, growing need due to increasing life expectancy. The Editorial team has maintained high standards and published original research papers, case reports and review articles from the best of the best contributors both national & international, consistently so that now, it has become a great tool in the hands of menopause practitioners.
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