Clear cell sarcoma arising from the iliac wing: case report

Clear cell sarcoma (CCS) is aggressive, slow growing tumor, arising from tendons, aponeuroses, and fascial structures. CCS compromises only 1% of soft tissue sarcomas. CCS is characterized by a high rate of local recurrence and distant metastasis. CCS is commonly located in extremities, and less likely to arise in the trunk with only rare cases found in pelvis or abdomen. Here we describe a case of clear cell sarcoma, in which it develops from the iliac wing with distant pulmonary and liver metastasis. We discuss and review the clinicopathologic features of CCS include: structural and microscopic characteristics, prognosis factors, management, and outcome.