Raghav Vadhul, Caroline S Halbach, Raymond G Areaux, Susan Berry, Joshua H Hou
{"title":"内皮功能障碍的儿童皮尔pearson骨髓-胰腺综合征处理Descemet剥离自动内皮角膜移植术使用缝线拉穿技术。","authors":"Raghav Vadhul, Caroline S Halbach, Raymond G Areaux, Susan Berry, Joshua H Hou","doi":"10.5693/djo.02.2019.09.001","DOIUrl":null,"url":null,"abstract":"<p><p>A 4-year-old girl with a history of Pearson marrow-pancreas syndrome presenting with severe, progressive photophobia was found to have bilateral, diffuse corneal thickening and peripheral pigmentary retinopathy. She underwent Descemet stripping automated endothelial keratoplasty (DSAEK) surgery in both eyes using a modified suture pull-through technique. Postoperatively there was no evidence of cataract formation or graft detachment; her corneas thinned, and her photophobia improved dramatically.</p>","PeriodicalId":38112,"journal":{"name":"Digital journal of ophthalmology : DJO","volume":" ","pages":"59-64"},"PeriodicalIF":0.0000,"publicationDate":"2019-11-17","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7001650/pdf/djo-19-040.pdf","citationCount":"3","resultStr":"{\"title\":\"Endothelial dysfunction in a child with Pearson marrow-pancreas syndrome managed with Descemet stripping automated endothelial keratoplasty using a suture pull-through technique.\",\"authors\":\"Raghav Vadhul, Caroline S Halbach, Raymond G Areaux, Susan Berry, Joshua H Hou\",\"doi\":\"10.5693/djo.02.2019.09.001\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>A 4-year-old girl with a history of Pearson marrow-pancreas syndrome presenting with severe, progressive photophobia was found to have bilateral, diffuse corneal thickening and peripheral pigmentary retinopathy. She underwent Descemet stripping automated endothelial keratoplasty (DSAEK) surgery in both eyes using a modified suture pull-through technique. Postoperatively there was no evidence of cataract formation or graft detachment; her corneas thinned, and her photophobia improved dramatically.</p>\",\"PeriodicalId\":38112,\"journal\":{\"name\":\"Digital journal of ophthalmology : DJO\",\"volume\":\" \",\"pages\":\"59-64\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2019-11-17\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7001650/pdf/djo-19-040.pdf\",\"citationCount\":\"3\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Digital journal of ophthalmology : DJO\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.5693/djo.02.2019.09.001\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2019/4/1 0:00:00\",\"PubModel\":\"eCollection\",\"JCR\":\"Q3\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Digital journal of ophthalmology : DJO","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5693/djo.02.2019.09.001","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2019/4/1 0:00:00","PubModel":"eCollection","JCR":"Q3","JCRName":"Medicine","Score":null,"Total":0}
Endothelial dysfunction in a child with Pearson marrow-pancreas syndrome managed with Descemet stripping automated endothelial keratoplasty using a suture pull-through technique.
A 4-year-old girl with a history of Pearson marrow-pancreas syndrome presenting with severe, progressive photophobia was found to have bilateral, diffuse corneal thickening and peripheral pigmentary retinopathy. She underwent Descemet stripping automated endothelial keratoplasty (DSAEK) surgery in both eyes using a modified suture pull-through technique. Postoperatively there was no evidence of cataract formation or graft detachment; her corneas thinned, and her photophobia improved dramatically.