乳果糖抢救:遗传性出血性毛细血管扩张患者中毒性肝性脑病由门静脉系统分流和鼻出血引起1例。

Case Reports in Hepatology Pub Date : 2019-03-26 eCollection Date: 2019-01-01 DOI:10.1155/2019/7573408
Ruchit N Shah, Michael Makar, Nasir Akhtar, Erin Forster
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引用次数: 5

摘要

遗传性出血性毛细血管扩张症(HHT)是一种罕见的常染色体显性遗传病,以毛细血管扩张和动静脉畸形为特征。涉及多个器官系统,包括皮肤、肺、胃肠道和大脑。肝性脑病是HHT的一种极其罕见的并发症,早期诊断和治疗可以挽救生命。我们报告一例罕见的肝性脑病,由hht诱导的门静脉系统分流引起,经乳果糖治疗。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia.

Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia.

Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia.

Hereditary hemorrhagic telangiectasia (HHT) is an uncommon autosomal dominant disorder characterized by telangiectasias and arteriovenous malformations. Multiple organ systems are involved including the skin, lungs, gastrointestinal tract, and brain. Hepatic encephalopathy is an extremely rare complication of HHT and early diagnosis and treatment can be life-saving. We present a rare case of hepatic encephalopathy caused by HHT-induced portosystemic shunting treated with lactulose.

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