重新定义脓毒症相关DIC的纤溶功能不全。

IF 4.1 2区 医学 Q2 HEMATOLOGY
Toshiaki Iba, Julie Helms, Cheryl L Maier, Ian Roberts
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引用次数: 0

摘要

脓毒症破坏凝血和纤溶之间的生理平衡,导致纤维蛋白形成超过纤维蛋白去除的状态,导致微血管血栓形成、器官衰竭和死亡。尽管内皮组织型纤溶酶原激活剂(t-PA)的早期爆发可能会短暂地增加纤溶酶的产生,但这一阶段会因纤溶酶原激活剂抑制剂-1 (PAI-1)的持续上调、可凝血酶激活的纤溶酶抑制剂的激活失调、内源性抗凝血剂的耗竭和进行性内皮病而迅速消失。除了抑制剂过量,新出现的证据表明纤溶酶原的定量缺陷是纤溶酶不足的主要原因。中性粒细胞胞外陷阱(NETs)含有弹性酶,它将纤溶酶原切割成无活性片段,减少功能性纤溶酶原的可用性,并损害纤维蛋白结合的纤溶酶的产生。当功能性纤溶酶原低于限速水平时,纤维蛋白表面不能有效地支持纤溶蛋白的形成,导致持续的微血管纤维蛋白沉积,尽管d -二聚体浓度升高。net -纤溶酶原轴将免疫血栓与“在脓毒症诱导的凝血病和明显弥散性血管内凝血(DIC)中观察到的纤溶性不全表型”联系起来。在临床上,低纤溶表现为高d -二聚体、PAI-1升高、纤溶酶生成减少以及粘弹性试验中纤溶活性低。包括t-PA或尿激酶挑战方案在内的整合生物标志物面板和粘弹性分析的多模式评估可能会改善风险分层。治疗策略主要针对凝血;然而,持续的低纤溶限制了它们的有效性。转化数据表明,在脓毒症患者和实验性DIC中,补充纤溶酶原可恢复功能性纤溶酶原水平,并使纤溶酶生成正常化,为纤溶酶定向治疗的概念提供了证据。未来的进展需要标准化的定义、功能性纤溶表型和表型引导的临床试验来恢复败血症的凝血-纤溶平衡。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Redefining Fibrinolytic Insufficiency in Sepsis-Associated DIC.

Sepsis disrupts the physiological balance between coagulation and fibrinolysis, resulting in a state in which fibrin formation exceeds fibrin removal and drives microvascular thrombosis, organ failure, and mortality. Although an early burst of endothelial tissue-type plasminogen activator (t-PA) may transiently increase plasmin generation, this phase is rapidly eclipsed by sustained upregulation of plasminogen activator inhibitor-1 (PAI-1), dysregulated activation of thrombin-activatable fibrinolysis inhibitor, depletion of endogenous anticoagulants, and progressive endotheliopathy. Beyond inhibitor excess, emerging evidence indicates that a quantitative defect in plasminogen is a central contributor to fibrinolytic insufficiency. Neutrophil extracellular traps (NETs) contain elastase, which cleaves plasminogen into inactive fragments, reducing functional plasminogen availability and impairing fibrin-bound plasmin generation. When functional plasminogen falls below rate-limiting levels, fibrin surfaces cannot efficiently support plasmin formation, resulting in persistent microvascular fibrin deposition despite elevated D-dimer concentrations. This NET-plasminogen axis links immunothrombosis to the "fibrinolytic insufficiency phenotype observed in sepsis-induced coagulopathy and overt disseminated intravascular coagulation (DIC)." Clinically, hypofibrinolysis is characterized by high D-dimers, elevated PAI-1, reduced plasmin generation, and low fibrinolytic activity on viscoelastic testing. Multimodal assessment integrating biomarker panels and viscoelastic assays, including t-PA- or urokinase-challenged protocols, may improve risk stratification. Therapeutic strategies largely targeted coagulation; however, persistent hypofibrinolysis limits their effectiveness. Translational data demonstrate that plasminogen supplementation restores functional plasminogen levels and normalizes plasmin generation in septic patients and in experimental DIC, providing proof of concept for fibrinolysis-directed therapy. Future progress requires standardized definitions, functional fibrinolytic phenotyping, and phenotype-guided clinical trials to restore the coagulo-fibrinolytic balance in sepsis.

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来源期刊
Seminars in thrombosis and hemostasis
Seminars in thrombosis and hemostasis 医学-外周血管病
CiteScore
8.80
自引率
21.10%
发文量
132
审稿时长
6-12 weeks
期刊介绍: Seminars in Thrombosis and Hemostasis is a topic driven review journal that focuses on all issues relating to hemostatic and thrombotic disorders. As one of the premiere review journals in the field, Seminars in Thrombosis and Hemostasis serves as a comprehensive forum for important advances in clinical and laboratory diagnosis and therapeutic interventions. The journal also publishes peer reviewed original research papers. Seminars offers an informed perspective on today''s pivotal issues, including hemophilia A & B, thrombophilia, gene therapy, venous and arterial thrombosis, von Willebrand disease, vascular disorders and thromboembolic diseases. Attention is also given to the latest developments in pharmaceutical drugs along with treatment and current management techniques. The journal also frequently publishes sponsored supplements to further highlight emerging trends in the field.
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