{"title":"中低收入国家以同性性青春期和双侧卵巢肿块为表现的先天性甲状腺功能减退症诊治面临的挑战:1例报告","authors":"Ashagre Gebremichael Ganta, Wintana Tesfaye Desta","doi":"10.1186/s12902-025-02058-0","DOIUrl":null,"url":null,"abstract":"<p><p>Congenital hypothyroidism (CH) is a prevalent condition that can lead to significant neurodevelopmental issues in infants if not diagnosed and treated promptly. Van Wyk and Grumbach Syndrome (VWGS), characterized by hypothyroidism, precocious puberty, and ovarian masses, is often misdiagnosed in low- and middle-income countries (LMICs) due to limited diagnostic resources. This case highlights systemic challenges, including delayed diagnosis and unnecessary surgical referrals.We present an 8-year-old girl diagnosed with Van Wyk-Grumbach syndrome, characterized by severe hypothyroidism, isosexual precocious puberty, and ovarian hyperstimulation. She exhibited symptoms including vaginal bleeding, abdominal distention, and marked obesity with stunted growth. Investigations revealed severe hypothyroidism (TSH: 96 mU/L) and enlarged bilateral ovarian cysts. After initiating levothyroxine therapy, the patient demonstrated remarkable clinical improvement, including reduced abdominal swelling and normalizing thyroid function. This case underscores the importance of considering hypothyroidism in differential diagnoses of ovarian masses in children, especially in regions lacking newborn screening protocols, to prevent unnecessary surgical interventions and ensure appropriate management of the condition.</p>","PeriodicalId":9152,"journal":{"name":"BMC Endocrine Disorders","volume":"25 1","pages":"234"},"PeriodicalIF":3.3000,"publicationDate":"2025-10-16","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC12532396/pdf/","citationCount":"0","resultStr":"{\"title\":\"Challenge faced in diagnosis and treatment of congenital hypothyroidism presenting with isosexual puberty and bilateral ovarian mass in low and middle income country: a case report.\",\"authors\":\"Ashagre Gebremichael Ganta, Wintana Tesfaye Desta\",\"doi\":\"10.1186/s12902-025-02058-0\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Congenital hypothyroidism (CH) is a prevalent condition that can lead to significant neurodevelopmental issues in infants if not diagnosed and treated promptly. Van Wyk and Grumbach Syndrome (VWGS), characterized by hypothyroidism, precocious puberty, and ovarian masses, is often misdiagnosed in low- and middle-income countries (LMICs) due to limited diagnostic resources. This case highlights systemic challenges, including delayed diagnosis and unnecessary surgical referrals.We present an 8-year-old girl diagnosed with Van Wyk-Grumbach syndrome, characterized by severe hypothyroidism, isosexual precocious puberty, and ovarian hyperstimulation. She exhibited symptoms including vaginal bleeding, abdominal distention, and marked obesity with stunted growth. Investigations revealed severe hypothyroidism (TSH: 96 mU/L) and enlarged bilateral ovarian cysts. After initiating levothyroxine therapy, the patient demonstrated remarkable clinical improvement, including reduced abdominal swelling and normalizing thyroid function. This case underscores the importance of considering hypothyroidism in differential diagnoses of ovarian masses in children, especially in regions lacking newborn screening protocols, to prevent unnecessary surgical interventions and ensure appropriate management of the condition.</p>\",\"PeriodicalId\":9152,\"journal\":{\"name\":\"BMC Endocrine Disorders\",\"volume\":\"25 1\",\"pages\":\"234\"},\"PeriodicalIF\":3.3000,\"publicationDate\":\"2025-10-16\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC12532396/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"BMC Endocrine Disorders\",\"FirstCategoryId\":\"3\",\"ListUrlMain\":\"https://doi.org/10.1186/s12902-025-02058-0\",\"RegionNum\":3,\"RegionCategory\":\"医学\",\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q3\",\"JCRName\":\"ENDOCRINOLOGY & METABOLISM\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"BMC Endocrine Disorders","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.1186/s12902-025-02058-0","RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"ENDOCRINOLOGY & METABOLISM","Score":null,"Total":0}
Challenge faced in diagnosis and treatment of congenital hypothyroidism presenting with isosexual puberty and bilateral ovarian mass in low and middle income country: a case report.
Congenital hypothyroidism (CH) is a prevalent condition that can lead to significant neurodevelopmental issues in infants if not diagnosed and treated promptly. Van Wyk and Grumbach Syndrome (VWGS), characterized by hypothyroidism, precocious puberty, and ovarian masses, is often misdiagnosed in low- and middle-income countries (LMICs) due to limited diagnostic resources. This case highlights systemic challenges, including delayed diagnosis and unnecessary surgical referrals.We present an 8-year-old girl diagnosed with Van Wyk-Grumbach syndrome, characterized by severe hypothyroidism, isosexual precocious puberty, and ovarian hyperstimulation. She exhibited symptoms including vaginal bleeding, abdominal distention, and marked obesity with stunted growth. Investigations revealed severe hypothyroidism (TSH: 96 mU/L) and enlarged bilateral ovarian cysts. After initiating levothyroxine therapy, the patient demonstrated remarkable clinical improvement, including reduced abdominal swelling and normalizing thyroid function. This case underscores the importance of considering hypothyroidism in differential diagnoses of ovarian masses in children, especially in regions lacking newborn screening protocols, to prevent unnecessary surgical interventions and ensure appropriate management of the condition.
期刊介绍:
BMC Endocrine Disorders is an open access, peer-reviewed journal that considers articles on all aspects of the prevention, diagnosis and management of endocrine disorders, as well as related molecular genetics, pathophysiology, and epidemiology.