Adnane El-Missioui, Fatima Zahra Benkarroum, Hind Ramdi
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引用次数: 0
摘要
乳突-左侧滴度综合征（PLS），也被称为牙周病伴掌跖角化病和“牙周病伴掌跖角化过度”，是一种罕见的常染色体隐性遗传病，以弥漫性掌跖角化病和侵袭性牙周炎为特征，导致乳牙和恒牙在很小的时候就过早脱落。本文的目的是重新审视PLS，解决其诊断更新和牙科管理，并提供深入了解在这种不寻常的疾病的病因的亲属迷人的作用。我们报告的情况下，两个摩洛哥姐妹5岁和8岁的PLS谁咨询了在CCTD在拉巴特的儿科学部门，摩洛哥，为早期的牙齿丢失。El-Missioui A, Benkarroum FZ, Ramdi H. papillon - lefvre综合征：两姐妹病例报告。中华临床儿科杂志，2015;18(6):733-737。
Papillon-Lefèvre Syndrome: Case Report of Two Sisters.
Papillon-Lefèvre syndrome (PLS), also known as keratosis palmoplantaris with periodontopathia and "hyperkeratosis palmoplantaris with periodontosis," is a rare autosomal recessive disorder, characterized by diffuse palmoplantar keratoderma and precocious aggressive periodontitis, leading to premature loss of deciduous and permanent dentition at a very young age. The aim of this article is to revisit PLS, address its diagnosis update and dental management, and to provide insight into the fascinating role of consanguinity in the etiology of this unusual illness. We report the case of two Moroccan sisters aged 5 and 8 years old with PLS who consulted the pedodontics department at the CCTD in Rabat, Morocco, for the early loss of teeth.
How to cite this article: El-Missioui A, Benkarroum FZ, Ramdi H. Papillon-Lefèvre Syndrome: Case Report of Two Sisters. Int J Clin Pediatr Dent 2025;18(6):733-737.
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