Nahid Afsar, A. K. M. Zahin, Md. Habib-E-Rasul, Md. Alfanuzzaman, A. M. Wadud Al Hasan
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Kartagener's Syndrome With Complications: Diagnostic Challenges in a Resource-Limited Setting
Kartagener's Syndrome (KS) is a rare genetic disorder characterized by bronchiectasis, chronic sinusitis, and situs inversus. This case report presents a 14-year-old girl from rural Bangladesh diagnosed with KS, who exhibited progressive respiratory distress, recurrent sinus infections, and primary amenorrhea. Diagnostic imaging revealed dextrocardia, bronchiectasis, and pulmonary hypertension. The patient was managed with oxygen therapy, chest physiotherapy, antibiotics, bronchodilators, diuretics, and hormonal support. This case highlights the challenges of diagnosing KS in low-resource settings and emphasizes the importance of early diagnosis and multidisciplinary care to prevent disease progression and improve patient outcomes.
期刊介绍：
Clinical Case Reports is different from other case report journals. Our aim is to directly improve global health and increase clinical understanding using case reports to convey important best practice information. We welcome case reports from all areas of Medicine, Nursing, Dentistry, and Veterinary Science and may include: -Any clinical case or procedure which illustrates an important best practice teaching message -Any clinical case or procedure which illustrates the appropriate use of an important clinical guideline or systematic review. As well as: -The management of novel or very uncommon diseases -A common disease presenting in an uncommon way -An uncommon disease masquerading as something more common -Cases which expand understanding of disease pathogenesis -Cases where the teaching point is based on an error -Cases which allow us to re-think established medical lore -Unreported adverse effects of interventions (drug, procedural, or other).
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