Panayotis K Vlachakis, Eva Nyktari, George Oikonomou, Anastasios Apostolos, Skevos Sideris, Konstantinos Toutouzas, Costas Tsioufis, Maria Drakopoulou
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A multifaceted clinical portrait of Ebstein's anomaly: a case series.
Background: It was in 1866 when Wilhelm Ebstein first described a rare case of a 19-year-old cyanotic patient with tricuspid valve regurgitation caused by a congenital malformation. Since then, Ebstein's anomaly (EA) has been recognized as a condition that exhibits a diverse clinical course with a formidable challenge for clinicians in terms of diagnosis, management, and prognosis.
Case summary: We present a case series of four patients with EA, shedding light on the varied clinical manifestations, treatment approaches, and outcomes that underscore the multifaceted nature of this condition.
Discussion: The management of EA requires a comprehensive and individualized approach in specialized centres. The cardiologists responsible for the long-term care of these patients are faced with various challenging 'dilemmas' in the clinical course of the disease at different stages. The evolving landscape of cardiology offers a promising avenue for improving the outcomes and quality of life of patients with EA.
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