成人Pancreatoblastoma。

IF 0.5 Q4 GASTROENTEROLOGY & HEPATOLOGY

ACG Case Reports Journal Pub Date : 2025-08-25 eCollection Date: 2025-08-01 DOI:10.14309/crj.0000000000001814

Thomas Gonzales, Sultan Mahmood, Saifur R Khan, Aatur Singhi

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引用次数: 0

摘要

胰腺母细胞瘤（PB）是一种极其罕见的胰腺组织恶性肿瘤，占所有胰腺肿瘤的不到1%。由于罕见的恶性肿瘤和潜在的多种鉴别诊断，成人发病的PB可能是具有挑战性的诊断。诊断成人PB的主要特征是组织学。约90%的病例可见鳞状小体。我们提出一个病例的患者诊断为成人发病的PB，谁提出了关键的临床和病理特征，以及罕见的特征，与恶性肿瘤相关。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

Adult-Onset Pancreatoblastoma.

查看原文本刊更多论文

Adult-Onset Pancreatoblastoma.

Pancreatoblastoma (PB), an extremely rare malignancy of the pancreatic tissue, comprises less than 1% of all pancreatic tumors. Owing to the rarity of the malignancy and the potential for multiple differential diagnoses, adult-onset PB can be challenging to diagnose. The hallmark characteristic in diagnosing adult PB is found histologically. In approximately 90% of cases, squamous corpuscles are observed. We present the case of a patient diagnosed with adult-onset PB, who presented with key clinical and pathological features, as well as rarer characteristics, associated with the malignancy.

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来源期刊

ACG Case Reports Journal GASTROENTEROLOGY & HEPATOLOGY-

自引率

14.30%

发文量

170

审稿时长

12 weeks

期刊介绍： ACG Case Reports Journal is a peer-reviewed, open-access publication that provides GI and hepatology fellows, private practice clinicians, and other healthcare providers an opportunity to share interesting case reports with their peers and with leaders in the field. ACG Case Reports Journal publishes case reports, images, videos and letters to the editor in all topics of gastroenterology and hepatology, including: Biliary Colon Endoscopy Esophagus Functional Bowel Disorders Inflammatory Bowel Disease Liver Nutrition and Obesity Pancreas Pathology Pediatric Small Bowel Stomach.