Paulo Victor de Jesus Silva, Leonardo Bernardes de Amaro, Guilherme Vieira Cavalcante, Jefferson Douglas Camargos Moreira, Wagner Eduardo Matheus
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引用次数: 0
摘要
Von Hippel-Lindau （VHL）病可引起附睾囊腺瘤，通常无症状。我们报告一位27岁男性VHL病史（切除中枢神经系统血管母细胞瘤），表现出异常的复发性血精和双侧附睾肿大。超声和CT证实双侧附睾病变和其他vhl相关发现（胰腺/肾脏）。持续血精提示双侧附睾切除术，确认乳头状囊腺瘤。本病例为非典型的vhl相关附睾囊腺瘤，需要手术治疗，而这些良性病变通常采用保守治疗。
VON Hippel-Lindau syndrome: A rare case of epididymal cystadenoma associated with hemospermia
Von Hippel-Lindau (VHL) disease can cause epididymal cystadenomas, typically asymptomatic. We report a 27-year-old male with a VHL history (resected CNS hemangioblastoma) presenting unusually with recurrent hemospermia and bilateral epididymal enlargement. Ultrasound and CT confirmed bilateral epididymal lesions and other VHL-associated findings (pancreatic/renal). Persistent hemospermia prompted bilateral epididymectomy, confirming papillary cystadenomas. This case highlights an atypical, symptomatic presentation of VHL-related epididymal cystadenoma requiring surgical intervention, contrasting with usual conservative management for these benign lesions.
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