{"title":"异位斜坡颅咽管瘤。","authors":"Golnaz Lotfian, Akram Al-Warqi, Santhosh Gaddikeri, Miral D Jhaveri, Surjith Vattoth","doi":"10.1007/s00234-025-03727-6","DOIUrl":null,"url":null,"abstract":"<p><p>Craniopharyngiomas are rare, benign tumors with a bimodal age distribution, typically found in children and older adults. They arise along the craniopharyngeal tract, often in the intra- or suprasellar regions, and may compress adjacent structures, causing diverse symptoms. Diagnosis is primarily MRI-based, revealing heterogeneous mass with cystic and solid elements. Chordoma, another rare tumor, arises from notochordal remnants, often in the sacrum or clivus, and displays distinct imaging characteristics like T2 hyperintensity and bony destruction. This report discusses a rare ectopic clival craniopharyngioma in an 11-year-old- the youngest case reported in the literature to our knowledge -extending from the sellar to the clival region. Noteworthy imaging findings included T1 hyperintensity and a downward growth pattern along the expected Rathke pouch course, helping distinguish it from chordoma.</p>","PeriodicalId":19422,"journal":{"name":"Neuroradiology","volume":" ","pages":""},"PeriodicalIF":2.6000,"publicationDate":"2025-08-07","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Ectopic clival craniopharyngioma.\",\"authors\":\"Golnaz Lotfian, Akram Al-Warqi, Santhosh Gaddikeri, Miral D Jhaveri, Surjith Vattoth\",\"doi\":\"10.1007/s00234-025-03727-6\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Craniopharyngiomas are rare, benign tumors with a bimodal age distribution, typically found in children and older adults. They arise along the craniopharyngeal tract, often in the intra- or suprasellar regions, and may compress adjacent structures, causing diverse symptoms. Diagnosis is primarily MRI-based, revealing heterogeneous mass with cystic and solid elements. Chordoma, another rare tumor, arises from notochordal remnants, often in the sacrum or clivus, and displays distinct imaging characteristics like T2 hyperintensity and bony destruction. This report discusses a rare ectopic clival craniopharyngioma in an 11-year-old- the youngest case reported in the literature to our knowledge -extending from the sellar to the clival region. Noteworthy imaging findings included T1 hyperintensity and a downward growth pattern along the expected Rathke pouch course, helping distinguish it from chordoma.</p>\",\"PeriodicalId\":19422,\"journal\":{\"name\":\"Neuroradiology\",\"volume\":\" \",\"pages\":\"\"},\"PeriodicalIF\":2.6000,\"publicationDate\":\"2025-08-07\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Neuroradiology\",\"FirstCategoryId\":\"3\",\"ListUrlMain\":\"https://doi.org/10.1007/s00234-025-03727-6\",\"RegionNum\":3,\"RegionCategory\":\"医学\",\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q2\",\"JCRName\":\"CLINICAL NEUROLOGY\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Neuroradiology","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.1007/s00234-025-03727-6","RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q2","JCRName":"CLINICAL NEUROLOGY","Score":null,"Total":0}
Craniopharyngiomas are rare, benign tumors with a bimodal age distribution, typically found in children and older adults. They arise along the craniopharyngeal tract, often in the intra- or suprasellar regions, and may compress adjacent structures, causing diverse symptoms. Diagnosis is primarily MRI-based, revealing heterogeneous mass with cystic and solid elements. Chordoma, another rare tumor, arises from notochordal remnants, often in the sacrum or clivus, and displays distinct imaging characteristics like T2 hyperintensity and bony destruction. This report discusses a rare ectopic clival craniopharyngioma in an 11-year-old- the youngest case reported in the literature to our knowledge -extending from the sellar to the clival region. Noteworthy imaging findings included T1 hyperintensity and a downward growth pattern along the expected Rathke pouch course, helping distinguish it from chordoma.
期刊介绍:
Neuroradiology aims to provide state-of-the-art medical and scientific information in the fields of Neuroradiology, Neurosciences, Neurology, Psychiatry, Neurosurgery, and related medical specialities. Neuroradiology as the official Journal of the European Society of Neuroradiology receives submissions from all parts of the world and publishes peer-reviewed original research, comprehensive reviews, educational papers, opinion papers, and short reports on exceptional clinical observations and new technical developments in the field of Neuroimaging and Neurointervention. The journal has subsections for Diagnostic and Interventional Neuroradiology, Advanced Neuroimaging, Paediatric Neuroradiology, Head-Neck-ENT Radiology, Spine Neuroradiology, and for submissions from Japan. Neuroradiology aims to provide new knowledge about and insights into the function and pathology of the human nervous system that may help to better diagnose and treat nervous system diseases. Neuroradiology is a member of the Committee on Publication Ethics (COPE) and follows the COPE core practices. Neuroradiology prefers articles that are free of bias, self-critical regarding limitations, transparent and clear in describing study participants, methods, and statistics, and short in presenting results. Before peer-review all submissions are automatically checked by iThenticate to assess for potential overlap in prior publication.