心下全异常肺静脉引流伴主动脉弓发育不全的早产儿:一个罕见而复杂的手术挑战。

IF 0.9 4区 医学 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS
Munavvar Gasimova, Bahruz Aliyev, Aynur Abbasaliyeva, Cabir Gulmaliyev, Khayala Mammadova, Shiraslan Bakhshaliyev
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引用次数: 0

摘要

完全性肺静脉异常引流伴主动脉弓发育不全是一种罕见而复杂的先天性心脏异常。我们报告一例13天大的晚期早产新生儿,表现为心下肺静脉引流完全异常,严重肺动脉高压和主动脉弓发育不全。患者接受了单期手术矫正,包括将肺静脉汇合处重新引至左心房,并在选择性脑灌注的体外循环下使用自体心包补片重建主动脉弓。术后恢复良好,拔管成功,肺动脉高压消退,解剖梗阻消失。本病例强调了早期、全面手术修复的可行性和有效性,以及多学科围手术期协调护理的必要性。长期随访对于监测功能结局和发现晚期并发症至关重要。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Infracardiac total anomalous pulmonary venous drainage with concomitant hypoplastic aortic arch in a preterm neonate: a rare and complex surgical challenge.

Total anomalous pulmonary venous drainage associated with hypoplastic aortic arch represents an exceptionally rare and intricate congenital cardiac anomaly. We report the case of a 13-day-old late preterm neonate presenting with infracardiac total anomalous pulmonary venous drainage, severe pulmonary hypertension, and a hypoplastic aortic arch. The patient underwent single-stage surgical correction involving rerouting of the pulmonary venous confluence to the left atrium and aortic arch reconstruction using autologous pericardial patch under cardiopulmonary bypass with selective cerebral perfusion. Postoperative recovery was favourable, marked by successful extubation, resolution of pulmonary hypertension, and absence of residual anatomical obstruction. This case highlights the feasibility and effectiveness of early, comprehensive surgical repair and the necessity of coordinated multidisciplinary perioperative care. Long-term follow-up remains vital for monitoring functional outcomes and detecting late complications.

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来源期刊
Cardiology in the Young
Cardiology in the Young 医学-小儿科
CiteScore
1.70
自引率
10.00%
发文量
715
审稿时长
4-8 weeks
期刊介绍: Cardiology in the Young is devoted to cardiovascular issues affecting the young, and the older patient suffering the sequels of congenital heart disease, or other cardiac diseases acquired in childhood. The journal serves the interests of all professionals concerned with these topics. By design, the journal is international and multidisciplinary in its approach, and members of the editorial board take an active role in the its mission, helping to make it the essential journal in paediatric cardiology. All aspects of paediatric cardiology are covered within the journal. The content includes original articles, brief reports, editorials, reviews, and papers devoted to continuing professional development.
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