{"title":"从横贯脊髓炎到髓圆锥综合征:小儿终末脑室进行性神经系统并发症1例报告","authors":"Reza Nejad Shahrokh Abadi , Farrokh Seilanian Toosi , Ahmadreza Mashreghi , Mehran Beiraghi Toosi , Hamid Khalesi , Narges Hashemi","doi":"10.1016/j.dscb.2025.100258","DOIUrl":null,"url":null,"abstract":"<div><div>Acute idiopathic Transverse Myelitis (TM) is a rare inflammatory spinal cord disorder distinguished with sensory deficits, autonomic dysfunction, and rapid onset muscle weakness, in the absence of direct infection, autoimmune disorders, or mass lesions. Conus Medullaris Syndrome (CMS) is another rare neurological condition affecting the distal segment of the spinal cord, seen as a rare complication of persistent cystic dilation of the Ventriculus Terminalis. In this report, we document the clinical and paraclinical findings of a seronegative patient initially presenting with TM, with incidental finding of Ventriculus Terminalis in Lumbar MRI, later complicating as CMS.</div></div>","PeriodicalId":72447,"journal":{"name":"Brain disorders (Amsterdam, Netherlands)","volume":"19 ","pages":"Article 100258"},"PeriodicalIF":0.0000,"publicationDate":"2025-07-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"From transverse myelitis to Conus Medullaris Syndrome: A pediatric case report of progressive neurological complications of Ventriculus Terminalis\",\"authors\":\"Reza Nejad Shahrokh Abadi , Farrokh Seilanian Toosi , Ahmadreza Mashreghi , Mehran Beiraghi Toosi , Hamid Khalesi , Narges Hashemi\",\"doi\":\"10.1016/j.dscb.2025.100258\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<div><div>Acute idiopathic Transverse Myelitis (TM) is a rare inflammatory spinal cord disorder distinguished with sensory deficits, autonomic dysfunction, and rapid onset muscle weakness, in the absence of direct infection, autoimmune disorders, or mass lesions. Conus Medullaris Syndrome (CMS) is another rare neurological condition affecting the distal segment of the spinal cord, seen as a rare complication of persistent cystic dilation of the Ventriculus Terminalis. In this report, we document the clinical and paraclinical findings of a seronegative patient initially presenting with TM, with incidental finding of Ventriculus Terminalis in Lumbar MRI, later complicating as CMS.</div></div>\",\"PeriodicalId\":72447,\"journal\":{\"name\":\"Brain disorders (Amsterdam, Netherlands)\",\"volume\":\"19 \",\"pages\":\"Article 100258\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2025-07-05\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Brain disorders (Amsterdam, Netherlands)\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://www.sciencedirect.com/science/article/pii/S2666459325000770\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Brain disorders (Amsterdam, Netherlands)","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S2666459325000770","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
From transverse myelitis to Conus Medullaris Syndrome: A pediatric case report of progressive neurological complications of Ventriculus Terminalis
Acute idiopathic Transverse Myelitis (TM) is a rare inflammatory spinal cord disorder distinguished with sensory deficits, autonomic dysfunction, and rapid onset muscle weakness, in the absence of direct infection, autoimmune disorders, or mass lesions. Conus Medullaris Syndrome (CMS) is another rare neurological condition affecting the distal segment of the spinal cord, seen as a rare complication of persistent cystic dilation of the Ventriculus Terminalis. In this report, we document the clinical and paraclinical findings of a seronegative patient initially presenting with TM, with incidental finding of Ventriculus Terminalis in Lumbar MRI, later complicating as CMS.