可乐定对僵硬人综合征危象的处理。

IF 4.8 2区 医学 Q1 CLINICAL NEUROLOGY
Salvatore Maria Lima, Nicasio Rini, Andrea Calì, Filippo Brighina, Vincenzo Di Stefano
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引用次数: 0

摘要

僵硬人综合征(SPS)是一种罕见的自身免疫性神经系统疾病,其特征是抗谷氨酸脱羧酶(GAD)抗体滴度高,gaba能抑制性神经传递受损。如果不及时治疗,SPS会发展为残疾,并伴有呼吸功能不全的高风险;因此,从一开始就采用最佳治疗方案是至关重要的,无论是在慢性还是在急性加重期间的紧急情况下。迄今为止,对于这种罕见疾病的治疗还没有明确的指导方针。在这项研究中,我们报告的情况下,妇女难治性SPS谁受益于可乐定与僵硬和SPS危机的立即解决影响。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Clonidine for the management of crises in stiff-person syndrome.

Stiff-person syndrome (SPS) is a rare autoimmune neurological disorder characterized by high titers of antibodies against glutamic acid decarboxylase (GAD) and impaired GABAergic inhibitory neurotransmission. If not promptly treated, SPS progresses to disability with high risk of respiratory insufficiency; therefore, it is essential to apply the best therapeutic regimens since the beginning, both in the chronic and in the emergency setting during exacerbations. To date, there are no defined guidelines for the treatment of this rare disease. In this study, we report the case of a woman affected by refractory SPS who benefited from clonidine with immediate resolution of stiffness and SPS crisis.

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来源期刊
Journal of Neurology
Journal of Neurology 医学-临床神经学
CiteScore
10.00
自引率
5.00%
发文量
558
审稿时长
1 months
期刊介绍: The Journal of Neurology is an international peer-reviewed journal which provides a source for publishing original communications and reviews on clinical neurology covering the whole field. In addition, Letters to the Editors serve as a forum for clinical cases and the exchange of ideas which highlight important new findings. A section on Neurological progress serves to summarise the major findings in certain fields of neurology. Commentaries on new developments in clinical neuroscience, which may be commissioned or submitted, are published as editorials. Every neurologist interested in the current diagnosis and treatment of neurological disorders needs access to the information contained in this valuable journal.
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