Ebstein异常中的房筋束通路：重新审视儿科术前EP研究的作用

IF 1.2 4区医学 Q3 CARDIAC & CARDIOVASCULAR SYSTEMS

Journal of electrocardiology Pub Date : 2025-06-16 DOI:10.1016/j.jelectrocard.2025.154053

Brock A. Karolcik MD, Lee B. Beerman MD, Christopher W. Follansbee MD, Gaurav Arora MD

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引用次数: 0

摘要

我们报告了一例6岁的Ebstein异常（EA）患者，在da Silva Cone修复（CR）之前的术前电生理研究（EPS）中发现右侧减小，仅顺行辅助通路（AP），推定为房束AP。心房血管性AP占AP的3%，但与EA相关。据我们所知，这是最年轻的EA合并心房血管性AP的病例。提供者应该意识到这种可能性，因为CRs在更年轻的患者中进行，并且可能在无症状的患者中发现。

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Atriofascicular pathway in Ebstein's anomaly: Revisiting the role of preoperative EP studies in pediatrics

We present a case of a 6-year-old with Ebstein's anomaly (EA) who was found to have a right lateral decremental, antegrade only accessory pathway (AP), presumed atriofascicular AP, during a pre-operative electrophysiology study (EPS) prior to da Silva Cone repair (CR). Atriofascicular APs represent <3 % of APs but have an association with EA. To the best of our knowledge, this is the youngest reported case of EA with an atriofascicular AP. Providers should be aware of this possibility, as CRs are being done at younger ages, and they may be discovered in asymptomatic patients.

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来源期刊

Journal of electrocardiology 医学-心血管系统

CiteScore

2.70

自引率

7.70%

发文量

152

审稿时长

38 days

期刊介绍： The Journal of Electrocardiology is devoted exclusively to clinical and experimental studies of the electrical activities of the heart. It seeks to contribute significantly to the accuracy of diagnosis and prognosis and the effective treatment, prevention, or delay of heart disease. Editorial contents include electrocardiography, vectorcardiography, arrhythmias, membrane action potential, cardiac pacing, monitoring defibrillation, instrumentation, drug effects, and computer applications.