{"title":"胱抑素C作为AL淀粉样变性患者肾脏预后评估的生物标志物。","authors":"Foteini Theodorakakou,Despina Fotiou,Filia Apostolakou,Ioannis Papassotiriou,Vasiliki Spiliopoulou,Ioannis Ntanasis-Stathopoulos,Panagiotis Malandrakis,Magdalini Migkou,Nikolaos Kanellias,Evangelos Eleutherakis-Papaiakovou,Erasmia Psimenou,Asimina Papanikolaou,Charikleia Gakiopoulou,Smaragdi Marinaki,Stavroula Giannouli,Maria Gavriatopoulou,Evangelos Terpos,Meletios-Athanasios Dimopoulos,Efstathios Kastritis","doi":"10.1002/ajh.27716","DOIUrl":null,"url":null,"abstract":"Cystatin C (CysC) has emerged as a novel and potentially more reliable biomarker for the estimation of glomerular filtration in the general population in patients with various conditions. In AL amyloidosis, the current renal staging system and renal response criteria are based on proteinuria and creatinine-based eGFR. We explored the prognostic role of CysC and of estimation of eGFR based on CysC-based equations in a cohort of 195 patients with newly diagnosed AL amyloidosis with renal involvement. Baseline CysC level was strongly and independently associated with progression to dialysis, and CysC levels ≥ 1.9 mg/L can be used in combination with the current renal staging system to identify patients with different risk of progression to dialysis among renal stages 2 and 3. eGFR based on CysC performed at least similarly to eGFR based on creatinine alone (by CKD-EPI race free formula) and the cutoff of 30 mL/min/1.73 m2 could better predict progression to dialysis at 2 years. At 6 months landmark, an increase in CysC by ≥ 1 mg/L was associated with higher risk of progression to dialysis (HR: 19.8, 95% CI 6.5-60.5, p < 0.001); a reduction of CysC based eGFR ≥ 30% was also associated with poor renal outcome, with a prognostic performance similar to current renal progression criteria. In conclusion, CysC provides prognostic information regarding the renal outcomes in patients with AL amyloidosis independently of the established biomarkers, but requires further validation.","PeriodicalId":7724,"journal":{"name":"American Journal of Hematology","volume":"16 1","pages":""},"PeriodicalIF":10.1000,"publicationDate":"2025-05-19","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Cystatin C as Biomarker for the Evaluation of Renal Outcome in AL Amyloidosis.\",\"authors\":\"Foteini Theodorakakou,Despina Fotiou,Filia Apostolakou,Ioannis Papassotiriou,Vasiliki Spiliopoulou,Ioannis Ntanasis-Stathopoulos,Panagiotis Malandrakis,Magdalini Migkou,Nikolaos Kanellias,Evangelos Eleutherakis-Papaiakovou,Erasmia Psimenou,Asimina Papanikolaou,Charikleia Gakiopoulou,Smaragdi Marinaki,Stavroula Giannouli,Maria Gavriatopoulou,Evangelos Terpos,Meletios-Athanasios Dimopoulos,Efstathios Kastritis\",\"doi\":\"10.1002/ajh.27716\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Cystatin C (CysC) has emerged as a novel and potentially more reliable biomarker for the estimation of glomerular filtration in the general population in patients with various conditions. In AL amyloidosis, the current renal staging system and renal response criteria are based on proteinuria and creatinine-based eGFR. We explored the prognostic role of CysC and of estimation of eGFR based on CysC-based equations in a cohort of 195 patients with newly diagnosed AL amyloidosis with renal involvement. Baseline CysC level was strongly and independently associated with progression to dialysis, and CysC levels ≥ 1.9 mg/L can be used in combination with the current renal staging system to identify patients with different risk of progression to dialysis among renal stages 2 and 3. eGFR based on CysC performed at least similarly to eGFR based on creatinine alone (by CKD-EPI race free formula) and the cutoff of 30 mL/min/1.73 m2 could better predict progression to dialysis at 2 years. At 6 months landmark, an increase in CysC by ≥ 1 mg/L was associated with higher risk of progression to dialysis (HR: 19.8, 95% CI 6.5-60.5, p < 0.001); a reduction of CysC based eGFR ≥ 30% was also associated with poor renal outcome, with a prognostic performance similar to current renal progression criteria. In conclusion, CysC provides prognostic information regarding the renal outcomes in patients with AL amyloidosis independently of the established biomarkers, but requires further validation.\",\"PeriodicalId\":7724,\"journal\":{\"name\":\"American Journal of Hematology\",\"volume\":\"16 1\",\"pages\":\"\"},\"PeriodicalIF\":10.1000,\"publicationDate\":\"2025-05-19\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"American Journal of Hematology\",\"FirstCategoryId\":\"3\",\"ListUrlMain\":\"https://doi.org/10.1002/ajh.27716\",\"RegionNum\":1,\"RegionCategory\":\"医学\",\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q1\",\"JCRName\":\"HEMATOLOGY\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"American Journal of Hematology","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.1002/ajh.27716","RegionNum":1,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q1","JCRName":"HEMATOLOGY","Score":null,"Total":0}
引用次数: 0
摘要
胱抑素C (Cystatin C, CysC)已成为一种新的、可能更可靠的生物标志物,可用于评估普通人群中各种疾病患者的肾小球滤过。在AL淀粉样变性中,目前的肾脏分期系统和肾脏反应标准是基于蛋白尿和肌酐为基础的eGFR。我们在195例新诊断的AL淀粉样变性伴肾脏受累患者队列中探讨了CysC和基于CysC的方程估计eGFR的预后作用。基线CysC水平与进展到透析有很强且独立的相关性,CysC水平≥1.9 mg/L可与现行的肾脏分期系统联合使用,以识别肾2期和肾3期患者进展到透析的不同风险。基于CysC的eGFR表现至少与单独基于肌酐的eGFR相似(通过CKD-EPI无竞赛公式),30 mL/min/1.73 m2的截止值可以更好地预测2年透析进展。在6个月里程碑时,CysC升高≥1 mg/L与进展为透析的高风险相关(HR: 19.8, 95% CI 6.5-60.5, p < 0.001);基于CysC的eGFR降低≥30%也与肾脏预后不良相关,其预后表现与目前的肾脏进展标准相似。总之,CysC为AL淀粉样变性患者的肾脏预后提供了独立于已建立的生物标志物的预后信息,但需要进一步验证。
Cystatin C as Biomarker for the Evaluation of Renal Outcome in AL Amyloidosis.
Cystatin C (CysC) has emerged as a novel and potentially more reliable biomarker for the estimation of glomerular filtration in the general population in patients with various conditions. In AL amyloidosis, the current renal staging system and renal response criteria are based on proteinuria and creatinine-based eGFR. We explored the prognostic role of CysC and of estimation of eGFR based on CysC-based equations in a cohort of 195 patients with newly diagnosed AL amyloidosis with renal involvement. Baseline CysC level was strongly and independently associated with progression to dialysis, and CysC levels ≥ 1.9 mg/L can be used in combination with the current renal staging system to identify patients with different risk of progression to dialysis among renal stages 2 and 3. eGFR based on CysC performed at least similarly to eGFR based on creatinine alone (by CKD-EPI race free formula) and the cutoff of 30 mL/min/1.73 m2 could better predict progression to dialysis at 2 years. At 6 months landmark, an increase in CysC by ≥ 1 mg/L was associated with higher risk of progression to dialysis (HR: 19.8, 95% CI 6.5-60.5, p < 0.001); a reduction of CysC based eGFR ≥ 30% was also associated with poor renal outcome, with a prognostic performance similar to current renal progression criteria. In conclusion, CysC provides prognostic information regarding the renal outcomes in patients with AL amyloidosis independently of the established biomarkers, but requires further validation.
期刊介绍:
The American Journal of Hematology offers extensive coverage of experimental and clinical aspects of blood diseases in humans and animal models. The journal publishes original contributions in both non-malignant and malignant hematological diseases, encompassing clinical and basic studies in areas such as hemostasis, thrombosis, immunology, blood banking, and stem cell biology. Clinical translational reports highlighting innovative therapeutic approaches for the diagnosis and treatment of hematological diseases are actively encouraged.The American Journal of Hematology features regular original laboratory and clinical research articles, brief research reports, critical reviews, images in hematology, as well as letters and correspondence.