遗传性癌症基因检测诊断骨髓增生异常综合征1例报告。

IF 4.7 2区 医学 Q1 GENETICS & HEREDITY
Sarah Ridd, Larissa Peck, Aniket Bankar, George S Charames, Jordan Lerner-Ellis, Radhika Mahajan, Peter J B Sabatini, Andrew Wong, Janet Malcolmson, Raymond H Kim
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引用次数: 0

摘要

实体瘤综合征的基因检测通常使用外周血白细胞(PBL)作为种系DNA的来源。这种方法在某些情况下有缺点,如体细胞镶嵌和血液恶性肿瘤。在这里,我们描述了一个病例,在PBL的种系基因检测显示了一个未经怀疑的骨髓增生异常综合征(MDS)的诊断。一名68岁男性,有三个实体瘤病史和明显的癌症家族史,接受了76基因遗传癌症小组的种系基因检测。PBL初步检测显示整个APC和CTNNA1基因缺失,提示5号染色体连续缺失(del(5q))。随后对培养成纤维细胞的检测结果为阴性,表明缺失是体细胞的。骨髓分析证实del(5q)的存在和MDS的诊断。本病例展示了通过遗传癌症基因检测发现血液病的潜力,强调了仔细解释结果、多学科随访和DNA来源选择的重要性。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Myelodysplastic syndrome diagnosed by genetic testing for hereditary cancer: a case report.

Genetic testing for solid tumor syndromes typically uses peripheral blood leukocytes (PBL) as the source of germline DNA. This approach has shortcomings in certain situations, such as somatic mosaicism and hematologic malignancies. Here we describe a case where germline genetic testing on PBL revealed an unsuspected diagnosis of myelodysplastic syndrome (MDS). A 68-year-old male with a history of three solid tumors and a significant family history of cancer underwent germline genetic testing with a 76-gene hereditary cancer panel. Initial testing using PBL revealed deletions of the entire APC and CTNNA1 genes, suggestive of a contiguous deletion of chromosome 5 (del(5q)). Subsequent testing on cultured fibroblasts was negative, indicating the deletions were somatic. Bone marrow analysis confirmed the presence of del(5q) and a diagnosis of MDS. This case demonstrates the potential to uncover hematologic disorders through hereditary cancer genetic testing, emphasizing the importance of careful results interpretation, multidisciplinary follow-up, and DNA source selection.

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来源期刊
NPJ Genomic Medicine
NPJ Genomic Medicine Biochemistry, Genetics and Molecular Biology-Molecular Biology
CiteScore
9.40
自引率
1.90%
发文量
67
审稿时长
17 weeks
期刊介绍: npj Genomic Medicine is an international, peer-reviewed journal dedicated to publishing the most important scientific advances in all aspects of genomics and its application in the practice of medicine. The journal defines genomic medicine as "diagnosis, prognosis, prevention and/or treatment of disease and disorders of the mind and body, using approaches informed or enabled by knowledge of the genome and the molecules it encodes." Relevant and high-impact papers that encompass studies of individuals, families, or populations are considered for publication. An emphasis will include coupling detailed phenotype and genome sequencing information, both enabled by new technologies and informatics, to delineate the underlying aetiology of disease. Clinical recommendations and/or guidelines of how that data should be used in the clinical management of those patients in the study, and others, are also encouraged.
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