IgG4相关疾病

G. Starita Fajardo , D. Lucena López , C. Arévalo-Cañas , A. González García
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引用次数: 0

摘要

igg4相关疾病(IgG4-RD)是一种免疫介导的纤维炎性疾病,几乎可以影响任何器官。最常见的表现是腺体受累、眼眶假瘤、胰腺受累和腹膜后纤维化。基于临床和组织学发现的2019年ACR/EULAR IgG4-RD分类标准可能对诊断有用。皮质类固醇是主要的治疗方法,尽管不同的免疫抑制药物正在研究中,结果不一。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Enfermedad relacionada con IgG4
IgG4-related disease (IgG4-RD) is an immune-mediated disorder of a fibroinflammatory nature that can affect practically any organ. Some of the most common manifestations are glandular involvement, orbital pseudotumor, pancreatic involvement, and retroperitoneal fibrosis. The 2019 ACR/EULAR classification criteria for IgG4-RD, based on clinical and histologic findings, may be useful for diagnosis. Corticosteroids are the mainstay of treatment, although different immunosuppressive drugs are under investigation with mixed results.
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