小儿盆腔肿块：一例罕见的骨外尤文氏肉瘤。

IF 2.1 3区医学 Q2 UROLOGY & NEPHROLOGY

Urology Pub Date : 2025-06-01 DOI:10.1016/j.urology.2025.03.038

Deepansh Dalela , Sarah Attia , Dinesh Rakheja , Shane Batie , Alexandra Carolan , Irina Stanasel

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引用次数: 0

摘要

尤文氏肉瘤（ES）是一种常见的儿童恶性骨肿瘤，但原发性骨外尤文氏肉瘤（EES）在骨盆区域尤为罕见。我们报告一个21个月大的男性与一个10厘米复杂的囊性肿块附着在膀胱。核心活检显示CD99、NKX2-2和EWSR1:ERG融合阳性的小圆细胞肿瘤。患者在诱导化疗后出现残留肿块，并行手术切除和前路清缝术，未累及其他盆腔器官。病理显示

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Pelvic Mass in a Pediatric Patient: A Rare Case of Extraosseous Ewing Sarcoma

Ewing sarcoma (ES) is a common malignant bone tumor in children, but primary extraosseous Ewing sarcoma (EES) in the pelvic region is particularly rare. We report a 21-month-old male with a 10-cm complex cystic mass adherent to the bladder. Core biopsy demonstrated a small round cell neoplasm positive for CD99, NKX2-2, and EWSR1:ERG fusion. The patient had a residual mass following induction chemotherapy, and underwent surgical resection with anterior detrusorrhaphy with no other pelvic organ involvement. Pathology showed <10% residual tumor with negative margins. Following completion of consolidation chemotherapy, imaging has shown no evidence of recurrent disease 13 months post-surgery.

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来源期刊

Urology 医学-泌尿学与肾脏学

CiteScore

3.30

自引率

9.50%

发文量

716

审稿时长

59 days

期刊介绍： Urology is a monthly, peer–reviewed journal primarily for urologists, residents, interns, nephrologists, and other specialists interested in urology The mission of Urology®, the "Gold Journal," is to provide practical, timely, and relevant clinical and basic science information to physicians and researchers practicing the art of urology worldwide. Urology® publishes original articles relating to adult and pediatric clinical urology as well as to clinical and basic science research. Topics in Urology® include pediatrics, surgical oncology, radiology, pathology, erectile dysfunction, infertility, incontinence, transplantation, endourology, andrology, female urology, reconstructive surgery, and medical oncology, as well as relevant basic science issues. Special features include rapid communication of important timely issues, surgeon''s workshops, interesting case reports, surgical techniques, clinical and basic science review articles, guest editorials, letters to the editor, book reviews, and historical articles in urology.