9个月大的卡萨巴赫-梅里特综合征1例：血管瘤罕见的并发症。

IF 0.8 4区医学 Q3 MEDICINE, GENERAL & INTERNAL

Journal of the Pakistan Medical Association Pub Date : 2025-03-01 DOI:10.47391/JPMA.11607

Hafiz Khalid Pervaiz, Usman Jamil Mughal, Izza Ali Rai, Mumtaz Touseef, Aliezeh Fatima Rai

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引用次数: 0

摘要

卡萨巴赫-梅里特现象（KMP）是一种危及生命的消耗性凝血病，常见于婴幼儿。它是血管病变扩大、血小板减少、微血管病溶血性贫血和低纤维蛋白血症的结合。一个9个月大的孩子谁提出了一个簇状血管瘤导致KMP的临床特征的情况下提出。在不同的表现阶段进行的调查和开始的药物治疗以及对治疗的特征反应也进行了讨论。

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A case of Kasabach-Merritt Syndrome in a nine-month-old: A rare complication of haemangioma in the young.

Kasabach-Merritt Phenomenon (KMP) is a life-threatening consumptive coagulopathy that commonly occurs in infants and young children. It is a combination of an enlarging vascular lesion, thrombocytopenia, microangiopathic haemolytic anaemia, and hypofibrinogemia. The case of a nine-month-old child who presented with a tuft haemangioma leading to the clinical features of KMP is presented. The investigation which was performed and pharmacological treatment initiated at different stages of presentation and the characteristic response to treatment are also discussed.

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来源期刊

Journal of the Pakistan Medical Association Medicine-General Medicine

CiteScore

1.10

自引率

11.10%

发文量

983

审稿时长

3-6 weeks

期刊介绍： Primarily being a medical journal, JPMA publishes scholarly research focusing on the various fields in the areas of health and medical education. It publishes original research describing recent advances in health particularly clinical studies, clinical trials, assessments of pathogens of diagnostic importance, medical genetics and epidemiological studies. Review articles highlighting importance of various issues in the domain of public health, drug research and medical education are also accepted. As a leading journal of South Asia, JPMA remains cognizant of the recent advances in the rapidly growing fields of biomedical sciences, it invites and encourages scholars to write short reviews and invited editorials on the emerging issues. We particularly aim to promote health standards of developing countries by encouraging manuscript submissions on issues affecting the public health and health delivery services.