Daniel Ahmed-Balestra, Martin Stattin, Katharina Krepler, Siamak Ansari-Shahrezaei
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Classification of acute retinal pigmentepithelitis.
Purpose: To present a pediatric case of acute retinal pigment epitheliitis (ARPE) and propose a classification based on imaging findings and prognosis.
Methods: A case report with literature review.
Results: The case demonstrated hallmark ARPE features alongside an atypical disease course, indicating a broader clinical spectrum. Multimodal imaging plays a crucial role in differentiating ARPE from mimicking retinal disorders.
Conclusion: ARPE may represent a spectrum of subtypes with varying prognostic implications. A classification based on age, laterality and imaging biomarkers could improve diagnostic accuracy and patient management.