Yuriy Y Kulyabin, Dmitriy S Zemel, Nataliya R Nichay, Alexey N Arkhipov, Darya A Dulceva, Ilya A Soynov
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Surgical Repair of the Aorta in a Neonate With Arterial Tortuosity Syndrome.
Arterial tortuosity syndrome (ATS) is an autosomal-recessive genetic connective tissue disorder that affects the aorta and medium-sized arterial vessels.1 We report a case of successful surgical management of the descending aorta in a ten-day-old patient with ATS who presented with multiorganic failure. The aortic reconstruction with a pulmonary homograft patch was performed using full-flow body perfusion.
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