肺动脉高压合并von Hippel-Lindau病的闭合性动脉导管再通及介入支架置入术1例

IF 0.9 4区医学 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS

Cardiology in the Young Pub Date : 2025-04-01 Epub Date: 2025-03-14 DOI:10.1017/S1047951125001374

Emine Gülşah Torun, Denizhan Bağrul, İbrahim Ece

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引用次数: 0

摘要

尽管医学治疗取得了进步，但肺动脉高压仍然是一种进行性、危及生命的疾病。我们报告了第一例通过封闭动脉导管支架植入反向Potts分流术的病例，该病例是一名四岁儿童，由于与Von Hippel-Lindau病相关的系统性肺动脉高压导致右心室衰竭，对三重抗肺动脉高压治疗无反应。手术后，患者的临床状况和超声心动图右心室收缩和舒张功能得到改善。

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Recanalization and interventional stenting of a closed ductus arteriosus in pulmonary hypertension associated with von Hippel-Lindau disease: a case report.

Pulmonary arterial hypertension remains a progressive, life-threatening condition despite advances in medical treatments. We report the first case of the interventional creation of a reverse Potts shunt by stenting a closed ductus arteriosus in a four-year-old child with right ventricular failure due to suprasystemic pulmonary arterial hypertension associated with Von Hippel-Lindau disease, unresponsive to triple anti-pulmonary arterial hypertension therapy. Following the procedure, the patient's clinical status and echocardiographic systolic and diastolic right ventricular function improved.

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来源期刊

Cardiology in the Young 医学-小儿科

CiteScore

1.70

自引率

10.00%

发文量

715

审稿时长

4-8 weeks

期刊介绍： Cardiology in the Young is devoted to cardiovascular issues affecting the young, and the older patient suffering the sequels of congenital heart disease, or other cardiac diseases acquired in childhood. The journal serves the interests of all professionals concerned with these topics. By design, the journal is international and multidisciplinary in its approach, and members of the editorial board take an active role in the its mission, helping to make it the essential journal in paediatric cardiology. All aspects of paediatric cardiology are covered within the journal. The content includes original articles, brief reports, editorials, reviews, and papers devoted to continuing professional development.