起源于鼻腔的多形性透明化血管扩张瘤：一例CARE病例报告

Q4 Medicine

Annales Francaises d''Oto-Rhino-Laryngologie et de Pathologie Cervico-Faciale Pub Date : 2025-02-01 DOI:10.1016/j.aforl.2025.01.003

S. Sun , D. Que , B. Pan , K. Hu

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引用次数: 0

摘要

多形性透明化血管扩张瘤（PHAT）是一种罕见的低级别恶性间质肿瘤。它通常发生在四肢和躯干，很少发生在头颈部。迄今为止，文献中仅报道了5例发生在头颈部的PHAT。PHAT的病因尚不清楚。我们根据CARE指南描述了一例鼻腔PHAT。一例32岁男性，原发于鼻腔的PHAT，两次手术后复发。第三次手术后行辅助放疗。定期随访36个月，未见肿瘤复发和转移。phat是一种罕见的软组织肿瘤，以其局部侵袭性而闻名。由于复发风险高，应实施广泛切除，如果由于靠近危险结构而不能完全切除，则可能通过放疗完成。

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Republication de : Pleomorphic hyalinizing angiectatic tumor originating in the nasal cavity: A CARE case report

Introduction

Pleomorphic hyalinizing angiectatic tumor (PHAT) is a rare low-grade malignant mesenchymal neoplasm. It commonly occurs in the limbs and trunk, with limited occurrences in the head and neck region. Only five cases of PHAT occurring in the head and neck have been reported in the literature to date. The etiology of PHAT remains unclear. We described a case of nasal cavity PHAT following CARE guidelines.

Case summary

A 32-year-old male with PHAT originating in the nasal cavity recurred after two surgeries. Adjuvant radiotherapy was performed after the third surgery. The patient has been regularly followed up for 36 months, and no tumor recurrence or metastasis has been observed.

Discussion

PHAT is a rare soft tissue tumor known for its local aggressiveness. Because of a high risk of recurrence, extensive resection should be implemented, possibly completed by radiotherapy if resection cannot be complete because of proximity to at-risk structures.

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来源期刊

Annales Francaises d''Oto-Rhino-Laryngologie et de Pathologie Cervico-Faciale Medicine-Otorhinolaryngology

CiteScore

0.10

自引率

0.00%

发文量

审稿时长

51 days