6月龄恶性外切间质瘤：罕见小儿肿瘤1例报告。

IF 2.1 3区医学 Q2 UROLOGY & NEPHROLOGY

Urology Pub Date : 2025-06-01 DOI:10.1016/j.urology.2025.01.056

Juanita Velasquez Ospina , Luciana Lerendegui , Paulo Moscardi , Daniel M. Tennenbaum , Liset Pelaez , Maggie E. Fader , Matthew D. Ramirez , Rafael Gosalbez

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引用次数: 0

摘要

恶性外切间质瘤是一种罕见的软组织肿瘤，同时包含间质和神经外胚层成分。我们提出的情况下，6个月大的男性腹部-盆腔肿块，最初诊断为胚胎横纹肌肉瘤。他对化疗和放疗反应不佳，随后手术完全切除证明肿瘤与恶性外切间质瘤相容。该病例强调了罕见肿瘤的诊断挑战、治疗复杂性和综合组织病理学评估的必要性。我们的目标是对有限的文献做出贡献，并强调个体化、多模式治疗方法的重要性。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Malignant Ectomesenchymoma in a 6-Month-Old: A Rare Pediatric Tumor Case Report

Malignant ectomesenchymoma is a rare type of soft tissue tumor that contains both mesenchymal and neuroectodermal components. We present the case of a 6-month-old male with an abdomino-pelvic mass, initially diagnosed as embryonal rhabdomyosarcoma. He had poor response to chemotherapy and radiotherapy, and subsequent complete surgical resection demonstrated the tumor to be compatible with malignant ectomesenchymoma. This case highlights the diagnostic challenges, treatment complexity, and need for comprehensive histopathological evaluation in rare tumors. We aim to contribute to the limited literature and emphasize the importance of individualized, multimodal treatment approaches.

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来源期刊

Urology 医学-泌尿学与肾脏学

CiteScore

3.30

自引率

9.50%

发文量

716

审稿时长

59 days

期刊介绍： Urology is a monthly, peer–reviewed journal primarily for urologists, residents, interns, nephrologists, and other specialists interested in urology The mission of Urology®, the "Gold Journal," is to provide practical, timely, and relevant clinical and basic science information to physicians and researchers practicing the art of urology worldwide. Urology® publishes original articles relating to adult and pediatric clinical urology as well as to clinical and basic science research. Topics in Urology® include pediatrics, surgical oncology, radiology, pathology, erectile dysfunction, infertility, incontinence, transplantation, endourology, andrology, female urology, reconstructive surgery, and medical oncology, as well as relevant basic science issues. Special features include rapid communication of important timely issues, surgeon''s workshops, interesting case reports, surgical techniques, clinical and basic science review articles, guest editorials, letters to the editor, book reviews, and historical articles in urology.