【儿童黑色素细胞肿瘤的诊断】。

Dermatologie (Heidelberg, Germany) Pub Date : 2025-03-01 Epub Date: 2025-01-27 DOI:10.1007/s00105-025-05471-7
Stephan Forchhammer, Valentin Aebischer
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引用次数: 0

摘要

儿童黑素细胞肿瘤的组织学诊断是具有挑战性的,因为良性痣往往类似于侵袭性肿瘤。准确的诊断对于早期发现罕见的儿童黑色素瘤至关重要。最近的进展已经建立了一种基于遗传背景的分类。这种分类区分了罕见的亚型,包括常规黑色素瘤、Spitz瘤和由先天性黑色素细胞痣引起的黑色素瘤。虽然最常见的Spitz肿瘤通常具有良好的预后,但传统黑色素瘤,特别是那些由先天性痣引起的黑色素瘤可能表现出与成人黑色素瘤相似的侵袭性病程。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
[Diagnosis of pediatric melanocytic tumors].

The histological diagnosis of pediatric melanocytic tumors is challenging, as benign nevi often resemble aggressive tumors. Accurate diagnosis is crucial for the early detection of rare pediatric melanomas. Recent advancements have established a classification based on genetic backgrounds. This classification distinguishes between rarer subtypes and includes groups such as conventional melanomas, Spitz tumors, and melanomas arising from congenital melanocytic nevi. While the most common group, Spitz tumors, generally has a favorable prognosis, conventional melanomas and especially those arising from congenital nevi may exhibit an aggressive course similar to that of adult melanoma.

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