IF 0.8 4区 医学 Q4 PEDIATRICS
World Journal of Pediatric Surgery Pub Date : 2024-12-31 eCollection Date: 2024-01-01 DOI:10.1136/wjps-2024-000916
Haley Etskovitz, Rosa S Kim, Sarah Ziqi Wang, Prathima Nandivada
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引用次数: 0

摘要

先天性巨结肠病(HSCR)是最常见的先天性肠道运动障碍,其特征是肌肠丛和粘膜下丛神经节细胞缺失,导致功能性肠梗阻。短节段巨结肠病(SS-HSCR)占大多数病例,手术切除是治疗的基石。尽管手术技术不断进步,但在手术时机、技术选择和切除的节结直肠袖的长度等方面,在实践中存在相当大的差异。本综述综合了SS-HSCR手术治疗的现有证据,讨论了技术特异性结果和未来研究的领域,重点是优化患者护理和功能结果。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Surgical management of short-segment Hirschsprung disease.

Hirschsprung disease (HSCR) is the most common congenital motility disorder of the intestine, characterized by the absence of ganglion cells in the myenteric and submucosal plexuses, leading to functional bowel obstruction. Short-segment Hirschsprung disease (SS-HSCR) accounts for the majority of cases, with surgical resection being the cornerstone of treatment. Despite advances in surgical techniques, considerable variability exists in practice regarding the timing of surgery, the choice of technique, and the length of aganglionic rectal cuff to resect. This review synthesizes the current evidence surrounding surgical management of SS-HSCR, discussing technique-specific outcomes and areas for future research, with a focus on optimizing patient care and functional outcomes.

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来源期刊
CiteScore
1.40
自引率
12.50%
发文量
38
审稿时长
13 weeks
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