胫盂旋转关节置换术治疗小儿Gorham-Stout病1例及手术技术。

Q4 Medicine

JBJS case connector Pub Date : 2024-12-05 eCollection Date: 2024-10-01 DOI:10.2106/JBJS.CC.24.00172

Emmanouil Grigoriou, M Bryant Transtrum, Scott Oishi, Charles E Johnston, Megan E Johnson

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引用次数: 0

摘要

病例：这是一个6岁的患者诊断为Gorham-Stout病（GSD），一种罕见的淋巴管性骨骼疾病，局限于左股骨。最初使用药物和支具进行非手术治疗失败。我们描述了一种明确的手术治疗方法，通过根治性股骨切除术和改良的旋转成形术，通过胫骨-骨盆旋转髋关节置换术。在2年的随访中，患者能够使用假肢装置行走。结论：改良旋转成形术是改善股骨GSD患者功能和生活质量的有效治疗方法。

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Tibiopelvic Rotational Arthroplasty for Pediatric Gorham-Stout Disease: A Case Report and Surgical Technique.

Case: This is a case of a 6-year-old patient diagnosed with Gorham-Stout disease (GSD), a rare lymphangiogenic skeletal disorder, localized to the left femur. Initial nonoperative treatment with pharmaceuticals and bracing was unsuccessful. We describe a definitive operative treatment with radical femoral resection and a modified rotationplasty technique through a tibiopelvic rotational hip arthroplasty. At 2-year follow-up, the patient was able to walk with a prosthetic device.

Conclusion: The use of this modified rotationplasty technique is an effective treatment option for patients with femoral GSD to improve function and quality of life.

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来源期刊

JBJS case connector Medicine-Medicine (all)

CiteScore

0.60

自引率

0.00%

发文量

319

期刊介绍： JBJS Case Connector helps improve patient care by providing the medical community with a journal that harnesses technology to provide information tools for discovery and reporting of unusual musculoskeletal problems, findings, treatment, and outcomes. Co-edited by Thomas W. Bauer, MD, PhD, and Ronald W. Lindsey, MD, JBJS Case Connector assists orthopaedic surgeons in the search for precedents, connections, and trends in their efforts to improve patient care. Using this unique journal, surgeons can find the commonalities between cases, benefit from the experience of their peers, and filter case information by many important variables in order to provide the best possible care for orthopaedic patients. This cross-referenced online journal includes thousands of orthopaedic case reports. It compiles symptoms, conditions, and demographic details to empower surgeons to find cases similar to theirs. Surgeons can mine the database to reveal emerging trends and identify patterns, distinguishing between truly rare cases and repeated, related single instances of a larger problem. The JBJS Case Connector Image Quiz feature provides interactive quizzes based on images from content published by JBJS and includes a discussion area for further exploration of ideas and concepts. The JBJS Image Quiz app for iPad and iPhone is available in the App Store. Contributions to JBJS Case Connector are welcomed from anywhere in the world and are considered on their merits. Articles must be written in English and should be submitted as outlined in the Instructions to Authors. All authors must abide by the JBJS ethics policies and all submissions to JBJS Case Connector are covered by the JBJS embargo policy.