一名长 QT 综合征 3 型患者因耦合间期极短的室性早搏诱发的电风暴

IF 1.3 4区医学 Q3 CARDIAC & CARDIOVASCULAR SYSTEMS

Journal of electrocardiology Pub Date : 2024-11-22 DOI:10.1016/j.jelectrocard.2024.153833

Akira Sato , Takuya Takahashi , Seiko Kuwata , Satoshi Nakano , Junichi Koizumi , Hirofumi Saiki , Manami Akasaka

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引用次数: 0

摘要

我们在此报告了一例患有长 QT3 型综合征（LQT3）的 10 岁男孩的病例，他出现了与短耦合时间室性心律失常（VASCT）相关的难治性抽搐（TdP）。更换植入式心律转复除颤器后，出现了电风暴，对高达 120 bpm 的心室起搏无反应。仔细检查心内电位后发现，TdP 与 VASCT 有关。右美托咪定和维拉帕米能有效控制 TdP，因此可以使用较慢的心室起搏。我们的病例凸显了在患有难治性 TdP 的 LQT3 患者中关注室性心律失常，尤其是那些耦联间期较短的室性心律失常的重要性。(99个字）。

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Electrical storm induced by premature ventricular beat with extremely short coupling interval in a patient with long QT syndrome type 3

Here we report the case of a 10-year-old boy with long QT syndrome type 3 (LQT3) who developed refractory torsade de pointes (TdP) associated with ventricular arrhythmia with a short coupling time (VASCT). After implantable cardioverter-defibrillator replacement, an electrical storm occurred, which was irresponsive to the ventricular pacing as high as 120 bpm. Close inspection of the intracardiac potential revealed TdP associated with VASCT. Dexmedetomidine and verapamil were effective in controlling TdP, which allowed management with slower ventricular pace. Our case highlights the importance of focusing on ventricular arrhythmias particularly those with short coupling interval, in LQT3 with refractory TdP. (99 words).

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来源期刊

Journal of electrocardiology 医学-心血管系统

CiteScore

2.70

自引率

7.70%

发文量

152

审稿时长

38 days

期刊介绍： The Journal of Electrocardiology is devoted exclusively to clinical and experimental studies of the electrical activities of the heart. It seeks to contribute significantly to the accuracy of diagnosis and prognosis and the effective treatment, prevention, or delay of heart disease. Editorial contents include electrocardiography, vectorcardiography, arrhythmias, membrane action potential, cardiac pacing, monitoring defibrillation, instrumentation, drug effects, and computer applications.