孤立性单侧肺动脉缺失（IUAPA）伴有进行性间质性阴影：病例报告。

IF 0.8 Q4 RESPIRATORY SYSTEM

Respirology Case Reports Pub Date : 2024-10-16 eCollection Date: 2024-10-01 DOI:10.1002/rcr2.70048

Tomohito Takeshige, Ryo Koyama, Makiko Kohmaru, Takashi Akimoto, Junko Watanabe, Toshifumi Yae, Kenji Kido, Kazuhisa Takahashi

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引用次数: 0

摘要

单侧肺动脉缺失（UAPA）是一种罕见的先天性疾病。如果单侧肺动脉缺失症不伴有先天性心脏病，则被称为孤立性单侧肺动脉缺失症（IUAPA）。单侧肺动脉缺失症通常在成年后才被诊断出来。一名 61 岁的女性患者因右胸痛和 9 年来不断恶化的间质性阴影而就诊。对比增强计算机断层扫描显示右肺肺动脉无血流，从而确诊为 IUAPA。在这个病例中，UAPA 的诊断是在大约 40 年后才确定的。本病例强调了在出现非特异性症状和间质性阴影的患者中，识别血管异常以鉴别这种疾病的重要性。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Isolated unilateral absence of the pulmonary artery (IUAPA) presenting with progressive interstitial shadows: A case report.

Unilateral absence of the pulmonary artery (UAPA) is a rare congenital condition. When UAPA occurs without associated congenital heart disease, it is referred to as isolated unilateral absence of the pulmonary artery (IUAPA). IUAPA is frequently not diagnosed until adulthood. A 61-year-old female patient presented with right chest pain and a worsening interstitial shadow over 9 years. Contrast-enhanced computed tomography revealed the absence of blood flow from the pulmonary artery in the right lung, leading to the diagnosis of IUAPA. In this case, the diagnosis of UAPA was established after approximately 40 years. This case underscores the importance of identifying vascular abnormalities to differentiate this condition in patients presenting with nonspecific symptoms and interstitial shadows.

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来源期刊

Respirology Case Reports RESPIRATORY SYSTEM-

CiteScore

1.40

自引率

0.00%

发文量

178

审稿时长

8 weeks

期刊介绍： Respirology Case Reports is an open-access online journal dedicated to the publication of original clinical case reports, case series, clinical images and clinical videos in all fields of respiratory medicine. The Journal encourages the international exchange between clinicians and researchers of experiences in diagnosing and treating uncommon diseases or diseases with unusual presentations. All manuscripts are peer-reviewed through a streamlined process that aims at providing a rapid turnaround time from submission to publication.