[神经纤维瘤病 1 型相关巨大丛状神经纤维瘤瘤内出血的紧急处理和围手术期策略]。

Q3 Medicine
Baochen Zhu, Yang Xiao, Ruiheng Liao, Hanxing Zhao, Xuewen Xu, Yan'ge Zhang
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引用次数: 0

摘要

目的综述1型神经纤维瘤病(NF1)相关巨型丛状神经纤维瘤(PNF)破裂的急诊处理和围手术期策略,为改善巨型PNF患者的治疗效果和生活质量提供系统的治疗方案:方法:对巨型丛状神经纤维瘤破裂和出血处理的文献进行回顾性研究,并根据临床经验对诊断、治疗和围手术期处理进行总结:通过实施综合诊断和治疗策略,包括早期诊断、影像学评估、紧急超选择性动脉栓塞和手术切除,可有效控制急性出血,同时降低术中大出血的风险,最大限度地减少术后并发症。因此,这种方法大大提高了治疗成功率和患者的生活质量:结论:对于与 NF1 相关的巨大 PNF 破裂,在多学科团队的协作下,采用急诊超选择性动脉栓塞联合手术切除,可有效提高治疗成功率,快速控制出血,缩小肿瘤体积,降低死亡率。今后的研究重点应放在评估接受破裂和出血巨大 PNF 治疗的患者的长期生活质量以及进一步优化治疗方案上。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
[Emergency management and perioperative strategies for intra-tumoral hemorrhage in neurofibromatosis type 1-related giant plexiform neurofibroma].

Objective: To review the emergency management and perioperative strategies for ruptured neurofibromatosis type 1 (NF1)-related giant plexiform neurofibroma (PNF), providing a systematic treatment protocol to improve the therapeutic outcomes and quality of life for patients with giant PNF.

Methods: The literature on the management of giant PNF rupture and hemorrhage was reviewed, and the diagnosis, treatment, and perioperative management were summarized based on clinical experiences.

Results: By implementing an integrated diagnostic and treatment strategy that includes early diagnosis, imaging evaluation, emergency ultra-selective arterial embolization combined with surgical excision, acute hemorrhage can be effectively controlled while also reducing the risk of major intraoperative bleeding and minimizing postoperative complications. As a result, this approach significantly improves treatment success rates and patient quality of life.

Conclusion: For ruptured NF1-related giant PNF, employing emergency ultra-selective arterial embolization combined with surgical excision, under the collaboration of a multidisciplinary team, can effectively improve treatment success rates, rapidly control bleeding, reduce tumor size, and lower mortality. Future research should focus on assessing the long-term quality of life of patients treated for ruptured and hemorrhaging giant PNF and on further optimizing treatment protocols.

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来源期刊
中国修复重建外科杂志
中国修复重建外科杂志 Medicine-Medicine (all)
CiteScore
0.80
自引率
0.00%
发文量
11334
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