胎儿左心发育不良综合征伴完整的心房隔膜：从胎儿期支架植入成功到次全支架闭塞--病例报告。

IF 1.6 3区医学 Q3 OBSTETRICS & GYNECOLOGY

Fetal Diagnosis and Therapy Pub Date : 2024-10-16 DOI:10.1159/000542069

Andreas Tulzer, Iris Scharnreitner, Eva Sames-Dolzer, Michaela Kreuzer, Rudolf Mair, Gerald Tulzer

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引用次数: 0

摘要

简介患有左心室发育不全综合征（HLHS）和完整房间隔（IAS）的胎儿总体预后较差，而且由于严重的继发性肺损伤，新生儿死亡的风险很高。为了让这些患者存活下来，我们在宫内为他们植入了房间隔支架：我们介绍了一例 HLHS 胎儿，其房间隔完整，有初期肉豆蔻肺的体征，在妊娠 30 周时成功放置了心房支架，但在接下来的几周内持续出现支架下梗阻：结论：放置的房间隔支架在分娩前持续阻塞是可能的，需要对成功治疗的胎儿进行密切监测。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Fetal Hypoplastic Left Heart Syndrome with Intact Atrial Septum: From Successful in utero Stenting to Subtotal Stent Occlusion - A Case Report.

Introduction: Fetuses with hypoplastic left heart syndrome (HLHS) and intact atrial septum (IAS) have an overall poor prognosis and a high risk of neonatal death due to severe secondary lung damage. Intrauterine stenting of the atrial septum was introduced in these patients to enable survival.

Case presentation: We present a case of a HLHS fetus with IAS and signs of incipient nutmeg lung, in whom at 30 weeks gestation an atrial stent was successfully placed but continuously developed subtotal stent-obstruction over the next weeks.

Conclusion: Continuous obstruction of placed atrial septum stents until delivery is possible and requires close monitoring of successfully treated fetuses.

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来源期刊

Fetal Diagnosis and Therapy 医学-妇产科学

CiteScore

4.70

自引率

9.10%

发文量

审稿时长

6-12 weeks

期刊介绍： The first journal to focus on the fetus as a patient, ''Fetal Diagnosis and Therapy'' provides a wide range of biomedical specialists with a single source of reports encompassing the common discipline of fetal medicine.