结缔组织病患者的缝线开裂:马凡综合征和魏尔-马切桑尼综合征。

M.M. Valentín-Pastrana Aguilar , I. Platas Moreno , N. Muñoz Sanz , B. Sandoval Cortés , J. Herrera Pereiro , I. Jiménez-Alfaro Morote
{"title":"结缔组织病患者的缝线开裂:马凡综合征和魏尔-马切桑尼综合征。","authors":"M.M. Valentín-Pastrana Aguilar ,&nbsp;I. Platas Moreno ,&nbsp;N. Muñoz Sanz ,&nbsp;B. Sandoval Cortés ,&nbsp;J. Herrera Pereiro ,&nbsp;I. Jiménez-Alfaro Morote","doi":"10.1016/j.oftale.2024.09.002","DOIUrl":null,"url":null,"abstract":"<div><div>Marfan and Weill-Marchesani syndromes have a mutation of the fibrillin gene (FBN1), producing alteration of connective tissue, within ophthalmology, it is important to take into consideration this type of diseases in cogenetic alterations in this system will produce modifications at the level of the ocular structures generating problems of various types, Most of the literature refers to ectopia lentis and the complications derived from it, as secondary glaucoma.</div><div>We present two patients, one with Marfan syndrome and the other with Weill-Marchesani syndrome, who developed lens dislocation, typical of their pathologies, which led them to undergo different surgeries. Both developed suture dehiscence after these surgeries, as a complication derived from their connective tissue involvement. We thus highlight the need for vigilance and extreme caution in the postoperative period of patients affected by this type of syndromes.</div></div>","PeriodicalId":93886,"journal":{"name":"Archivos de la Sociedad Espanola de Oftalmologia","volume":"99 11","pages":"Pages 512-516"},"PeriodicalIF":0.0000,"publicationDate":"2024-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Suture dehiscence in patients with connective tissue disease: Marfan and Weill-Marchesani syndromes\",\"authors\":\"M.M. Valentín-Pastrana Aguilar ,&nbsp;I. Platas Moreno ,&nbsp;N. Muñoz Sanz ,&nbsp;B. Sandoval Cortés ,&nbsp;J. Herrera Pereiro ,&nbsp;I. Jiménez-Alfaro Morote\",\"doi\":\"10.1016/j.oftale.2024.09.002\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<div><div>Marfan and Weill-Marchesani syndromes have a mutation of the fibrillin gene (FBN1), producing alteration of connective tissue, within ophthalmology, it is important to take into consideration this type of diseases in cogenetic alterations in this system will produce modifications at the level of the ocular structures generating problems of various types, Most of the literature refers to ectopia lentis and the complications derived from it, as secondary glaucoma.</div><div>We present two patients, one with Marfan syndrome and the other with Weill-Marchesani syndrome, who developed lens dislocation, typical of their pathologies, which led them to undergo different surgeries. Both developed suture dehiscence after these surgeries, as a complication derived from their connective tissue involvement. We thus highlight the need for vigilance and extreme caution in the postoperative period of patients affected by this type of syndromes.</div></div>\",\"PeriodicalId\":93886,\"journal\":{\"name\":\"Archivos de la Sociedad Espanola de Oftalmologia\",\"volume\":\"99 11\",\"pages\":\"Pages 512-516\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2024-11-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Archivos de la Sociedad Espanola de Oftalmologia\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://www.sciencedirect.com/science/article/pii/S2173579424001609\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Archivos de la Sociedad Espanola de Oftalmologia","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S2173579424001609","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0

摘要

马凡综合征和魏尔-马切萨尼综合征的纤维蛋白基因(FBN1)发生突变,导致结缔组织发生改变,在眼科领域,必须考虑到这类疾病,因为该系统的遗传改变会导致眼部结构发生改变,从而引发各种问题。我们介绍了两名患者,一名患有马凡氏综合征,另一名患有魏尔-马切萨尼综合征,他们都出现了晶状体脱位,这是他们的典型病症,导致他们接受了不同的手术。两人在手术后都出现了缝线开裂,这是结缔组织受累引起的并发症。因此,我们强调在此类综合征患者的术后阶段需要保持警惕和格外小心。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Suture dehiscence in patients with connective tissue disease: Marfan and Weill-Marchesani syndromes
Marfan and Weill-Marchesani syndromes have a mutation of the fibrillin gene (FBN1), producing alteration of connective tissue, within ophthalmology, it is important to take into consideration this type of diseases in cogenetic alterations in this system will produce modifications at the level of the ocular structures generating problems of various types, Most of the literature refers to ectopia lentis and the complications derived from it, as secondary glaucoma.
We present two patients, one with Marfan syndrome and the other with Weill-Marchesani syndrome, who developed lens dislocation, typical of their pathologies, which led them to undergo different surgeries. Both developed suture dehiscence after these surgeries, as a complication derived from their connective tissue involvement. We thus highlight the need for vigilance and extreme caution in the postoperative period of patients affected by this type of syndromes.
求助全文
通过发布文献求助,成功后即可免费获取论文全文。 去求助
来源期刊
自引率
0.00%
发文量
0
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
确定
请完成安全验证×
copy
已复制链接
快去分享给好友吧!
我知道了
右上角分享
点击右上角分享
0
联系我们:info@booksci.cn Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。 Copyright © 2023 布克学术 All rights reserved.
京ICP备2023020795号-1
ghs 京公网安备 11010802042870号
Book学术文献互助
Book学术文献互助群
群 号:481959085
Book学术官方微信