横膈膜卡斯特曼氏病:一种罕见的淋巴增生性疾病:临床和放射学视角

Q4 Medicine
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引用次数: 0

摘要

卡斯特曼病(CD)是一种罕见的良性非克隆性淋巴细胞增生性疾病,病因不清,由于其非特异性特征,给诊断带来了巨大挑战。CD分为单中心型(UCD)和多中心型(MCD),其中MCD又分为HHV-8相关型和特发性(iMCD)型。临床表现包括发热、体重减轻、盗汗和器官肿大,具体症状取决于亚型。CD 的诊断标准包括主要标准(组织病理学检查)和次要标准。包括 CT、MRI 和 PET-CT 在内的影像学技术在诊断、分期和与其他疾病鉴别方面起着至关重要的作用。本文讨论了 CD 的病理生理学、临床特征、诊断标准和影像学发现,并以一例偶然发现右心房肿块的肾病患者为例进行说明。该病例强调了综合影像学和临床评估在治疗 CD 方面的重要性。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Diaphragmatic Castleman's disease: A rare lymphoproliferative disorder: Clinical and radiological perspectives
Castleman's disease (CD) is a rare, benign nonclonal lymphoproliferative disorder with an unclear etiology, presenting significant diagnostic challenges due to its nonspecific features. CD is categorized into unicentric (UCD) and multicentric (MCD) types, with MCD further divided into HHV-8-associated and idiopathic (iMCD) forms. Clinical manifestations include fever, weight loss, night sweats, and organomegaly, with specific symptoms depending on the subtype. Diagnostic criteria for CD involve a combination of major criteria-histopathologic examination and minor criteria. Imaging techniques, including CT, MRI, and PET-CT, play a crucial role in diagnosis, staging, and differentiation from other diseases. This paper discusses the pathophysiology, clinical features, diagnostic criteria, and imaging findings of CD, illustrated by a case of a patient with renal disease with incidentally detected a right cardiophrenic mass. The case highlights the importance of comprehensive imaging and clinical evaluation in managing CD.
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来源期刊
Radiology Case Reports
Radiology Case Reports Medicine-Radiology, Nuclear Medicine and Imaging
CiteScore
1.10
自引率
0.00%
发文量
1074
审稿时长
30 days
期刊介绍: The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.
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