系统性红斑狼疮内脏肌肉运动障碍综合征:18 氟脱氧葡萄糖正电子发射断层扫描-计算机断层扫描的作用是什么?一个临床病例和文献综述。

IF 1.2 Q4 RHEUMATOLOGY
S Scriffignano, F M Perrotta, M Ricci, B Carabellese, E Lubrano
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引用次数: 0

摘要

内脏肌肉运动障碍综合征(VMDS)是系统性红斑狼疮(SLE)临床病程中描述的一种罕见综合征。其特征是肠壁弥漫性增厚,胃肠道-生殖泌尿道-肝胆中空内脏扩张和运动障碍。由于该综合征临床特征的罕见性和异质性,目前尚不完全清楚哪种影像诊断技术最适合诊断和/或随访,尽管在所有已描述的病例中,计算机断层扫描(CT)通常用于研究内脏受累情况。然而,目前还没有通过 18 氟脱氧葡萄糖(18FDG)- 正电子发射计算机断层扫描(18FDG-PET-CT)来描述内脏代谢活动的病例。在此,我们报告了首例通过 18FDG-PET-CT 研究 VMDS 的临床病例,描述了这种罕见综合征在系统性红斑狼疮发作期间的代谢活动。我们发现患者的肠道代谢负担较重,十二指肠固定过度,肝脏代谢活性较高。此外,我们还回顾了有关系统性红斑狼疮 VMDS 的文献,重点关注不同解剖部位(肠道、泌尿道、胆管)的成像技术、患者症状和治疗方法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Visceral muscle dysmotility syndrome in systemic lupus erythematosus: which is the role of 18 fluorodeoxyglucose-positron emission tomography-computed tomography? A clinical case and literature review.

Visceral muscle dysmotility syndrome (VMDS) is a rare syndrome, described in the systemic lupus erythematosus (SLE) clinical course. It is characterized by diffuse thickened intestinal wall and gastrointestinal-genitourinary-hepatobiliary hollow viscera dilatation and dysmotility. Due to the rarity and the heterogeneity of the clinical characteristics of this syndrome, it is not entirely clear which is the best diagnostic imaging technique for the diagnosis and/or follow-up, even if, in all the described cases, computed tomography (CT) was generally used to study visceral involvement. However, there are no cases describing the visceral metabolic activity by 18 fluorodeoxyglucose (18FDG)-positron emission tomography-CT (18FDG-PET-CT). Here, we reported the first clinical case of VMDS studied by 18FDG-PET-CT, characterizing the metabolic activity of this rare syndrome during SLE flare. We found a high intestinal metabolic burden, hyper-fixation in duodenum, and high hepatic metabolic activity. Moreover, we reviewed the literature on VMDS in SLE, focusing on imaging techniques in different anatomical sites (bowel, urinary tract, bile ducts), patients' symptoms, and treatment.

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来源期刊
Reumatismo
Reumatismo RHEUMATOLOGY-
CiteScore
2.10
自引率
7.10%
发文量
20
审稿时长
10 weeks
期刊介绍: Reumatismo is the official Journal of the Italian Society of Rheumatology (SIR). It publishes Abstracts and Proceedings of Italian Congresses and original papers concerning rheumatology. Reumatismo is published quarterly and is sent free of charge to the Members of the SIR who regularly pay the annual fee. Those who are not Members of the SIR as well as Corporations and Institutions may also subscribe to the Journal.
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