表现为局部多灶性 GGOs 的自身免疫性肺泡蛋白沉着症：病例报告

Q4 Medicine

Radiology Case Reports Pub Date : 2024-09-20 DOI:10.1016/j.radcr.2024.08.097

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引用次数: 0

摘要

肺泡蛋白沉积症（PAP）是一种罕见疾病，其特点是肺泡内表面活性物质堆积。胸部薄层计算机断层扫描（TSCT）上的疯狂铺路外观是这种疾病的特征。我们报告了一例不寻常的 PAP 病例，患者是一名 80 岁的女性，在 TSCT 上表现为多个局部磨玻璃不透明斑（GGOs）。由于其中一个位于右肺顶端的病灶增大，因此被怀疑是肺腺癌。然而，在随访期间，其他病灶都变小了。患者接受了右肺上叶切除术，经组织学检查确诊为肺腺癌。在出现多个局部 GGOs 的病例中，即使具有疯狂铺路样外观的 GGOs 是以小叶而非弥漫的方式分布，也应考虑为 PAP。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Autoimmune pulmonary alveolar proteinosis presenting as localized multifocal GGOs: A case report

Pulmonary alveolar proteinosis (PAP) is a rare disease, which is characterized by the alveolar accumulation of surfactant. A crazy-paving appearance on chest thin-section computed tomography (TSCT) is a characteristic feature of this disease. We report an unusual case of PAP, which presented as multiple localized ground glass opacites (GGOs) on TSCT in an 80-year-old female. As one of these lesions at the apex of the right lung increased in size, it was suspected to be a pulmonary adenocarcinoma. However, the others became smaller during the follow-up period. Right upper lobectomy was performed, and PAP was histologically diagnosed. In cases exhibiting multiple localized GGOs, PAP should be considered, even if GGOs with a crazy-paving-like appearance are distributed in a lobular rather than diffuse manner.

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来源期刊

Radiology Case Reports Medicine-Radiology, Nuclear Medicine and Imaging

CiteScore

1.10

自引率

0.00%

发文量

1074

审稿时长

30 days

期刊介绍： The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.